Hypohydrotic Ectodermal Dysplasia: A Clinical Case

Ectodermal dysplasia is a rare inherited disorder distinguished by the not normal development of certain structures of ectodermal origin. The hypohydrotic ectodermal dysplasia has an autosomal recessive or X-linked inheritance, the latter being the most frequent. Patients with ectodermal dysplasia a...

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Autores principales: Mercado, Silvia, Caciva, Ricardo
Formato: Artículo revista
Lenguaje:Español
Publicado: Facultad de Odontología 2019
Materias:
dentistry, hypohydrotic ectodermal dysplasia, patient management
odontología, displasia ectodérmica hipohidrótica, manejo paciente
Acceso en línea:https://revistas.unc.edu.ar/index.php/RevFacOdonto/article/view/26911
Aporte de:
Revista de la Facultad de Odontología de Universidad Nacional de Córdoba
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spelling I10-R335-article-269112019-12-20T08:52:50Z Hypohydrotic Ectodermal Dysplasia: A Clinical Case Displasia ectodérmica hipohidrótica: un caso clínico Mercado, Silvia Caciva, Ricardo dentistry, hypohydrotic ectodermal dysplasia, patient management odontología, displasia ectodérmica hipohidrótica, manejo paciente Ectodermal dysplasia is a rare inherited disorder distinguished by the not normal development of certain structures of ectodermal origin. The hypohydrotic ectodermal dysplasia has an autosomal recessive or X-linked inheritance, the latter being the most frequent. Patients with ectodermal dysplasia are patients who require a multidisciplinary approach to their treatment. It is of great importance that the patient is treated at an early age so that their self-esteem and their integration into society are not affected. Due to the oral characteristics of the DEH, the most common treatment is the elaboration of total prostheses, although the clinician may face various difficulties such as the poor development of alveolar processes and dry mouth, resulting from the poor or no salivary secretion. La displasia ectodérmica es un raro desorden hereditario distinguido por un desarrollo anormal de ciertas estructuras de origen ectodérmico. La displasia ectodérmica hipohidrótica presenta una herencia autosómica recesiva o ligada al cromosoma X, siendo esta última la más frecuente. Los pacientes con displasia ectodérmica son pacientes que requieren un enfoque multidisciplinario en su tratamiento. Es de gran importancia que el paciente sea atendido a una edad temprana para que no se vea afectada su autoestima y su integración a la sociedad. Debido a las características bucales de la DEH el tratamiento más concurrido es la elaboración de prótesis totales, aunque el clínico puede enfrentar a diversas dificultades como el pobre desarrollo de los procesos alveolares y a la resequedad bucal, consecuente de la pobre o nula secreción salival. Facultad de Odontología 2019-12-20 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf https://revistas.unc.edu.ar/index.php/RevFacOdonto/article/view/26911 Revista de la Facultad de Odontología; Vol. 29 Núm. 3 (2019): Volumen 29 número 3; 25-30 2545-7594 0325-1071 spa https://revistas.unc.edu.ar/index.php/RevFacOdonto/article/view/26911/28577
institution Universidad Nacional de Córdoba
institution_str I-10
repository_str R-335
container_title_str Revista de la Facultad de Odontología
language Español
format Artículo revista
topic dentistry, hypohydrotic ectodermal dysplasia, patient management
odontología, displasia ectodérmica hipohidrótica, manejo paciente
spellingShingle dentistry, hypohydrotic ectodermal dysplasia, patient management
odontología, displasia ectodérmica hipohidrótica, manejo paciente
Mercado, Silvia
Caciva, Ricardo
Hypohydrotic Ectodermal Dysplasia: A Clinical Case
topic_facet dentistry, hypohydrotic ectodermal dysplasia, patient management
odontología, displasia ectodérmica hipohidrótica, manejo paciente
author Mercado, Silvia
Caciva, Ricardo
author_facet Mercado, Silvia
Caciva, Ricardo
author_sort Mercado, Silvia
title Hypohydrotic Ectodermal Dysplasia: A Clinical Case
title_short Hypohydrotic Ectodermal Dysplasia: A Clinical Case
title_full Hypohydrotic Ectodermal Dysplasia: A Clinical Case
title_fullStr Hypohydrotic Ectodermal Dysplasia: A Clinical Case
title_full_unstemmed Hypohydrotic Ectodermal Dysplasia: A Clinical Case
title_sort hypohydrotic ectodermal dysplasia: a clinical case
description Ectodermal dysplasia is a rare inherited disorder distinguished by the not normal development of certain structures of ectodermal origin. The hypohydrotic ectodermal dysplasia has an autosomal recessive or X-linked inheritance, the latter being the most frequent. Patients with ectodermal dysplasia are patients who require a multidisciplinary approach to their treatment. It is of great importance that the patient is treated at an early age so that their self-esteem and their integration into society are not affected. Due to the oral characteristics of the DEH, the most common treatment is the elaboration of total prostheses, although the clinician may face various difficulties such as the poor development of alveolar processes and dry mouth, resulting from the poor or no salivary secretion.
publisher Facultad de Odontología
publishDate 2019
url https://revistas.unc.edu.ar/index.php/RevFacOdonto/article/view/26911
work_keys_str_mv AT mercadosilvia hypohydroticectodermaldysplasiaaclinicalcase
AT cacivaricardo hypohydroticectodermaldysplasiaaclinicalcase
AT mercadosilvia displasiaectodermicahipohidroticauncasoclinico
AT cacivaricardo displasiaectodermicahipohidroticauncasoclinico
first_indexed 2024-09-03T21:15:45Z
last_indexed 2024-09-03T21:15:45Z
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