Dermatofibrosarcoma protuberans treated with Mohs surgery: case report

Objectives: Dermatofibrosarcoma protuberans is a sarcomatous neoplasm with low incidence. It exhibits slow growth; however, it has the capacity to involve deep tissues. Clinically, it can mimic benign lesions, presenting as thickened or atrophic plaques that slowly transform into protruding lesions...

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Autores principales: Abeledo, Lía Salomé, Barbini, Carla, Russier, Gerardo, Busso, Corina
Formato: Artículo revista
Lenguaje:Español
Publicado: Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2025
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Acceso en línea:https://revistas.unc.edu.ar/index.php/med/article/view/45363
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spelling I10-R327-article-453632025-04-21T16:09:45Z Dermatofibrosarcoma protuberans treated with Mohs surgery: case report Dermatofibrosarcoma protuberans tratado con cirugía de Mohs: reporte de un caso Dermatofibrosarcoma protuberante tratado com cirurgia de Mohs: relatório de um caso Abeledo, Lía Salomé Barbini, Carla Russier, Gerardo Busso, Corina Barbini, Carla Russier, Gerardo Busso, Corina Barbini, Carla Russier, Gerardo Busso, Corina dermatofibrosarcoma mohs surgery sarcoma dermatofibrosarcoma cirugía de mohs sarcoma dermatofibrossarcoma cirurgia de mohs sarcoma Objectives: Dermatofibrosarcoma protuberans is a sarcomatous neoplasm with low incidence. It exhibits slow growth; however, it has the capacity to involve deep tissues. Clinically, it can mimic benign lesions, presenting as thickened or atrophic plaques that slowly transform into protruding lesions. The treatment of choice is surgical excision, with Mohs micrographic surgery standing out for its advantages. Clinical case: A 40-year-old male patient with dermatofibrosarcoma protuberans on the back underwent excision using the Mohs technique, with no tumor recurrence after two years of follow-up. Conclusion: It is important to highlight that the Mohs technique offers advantages over conventional methods, allowing for tissue optimization, ensuring clear margins, and achieving a low recurrence rate Objetivos: El dermatofibrosarcoma protuberans es una neoplasia sarcomatosa de baja incidencia. Presenta un crecimiento lento, sin embargo, tiene la capacidad de comprometer los tejidos profundos. Clínicamente pueden simular lesiones benignas, se presenta como placas engrosadas o atróficas, que lentamente se transforman en lesiones protuberantes. Se plantea como tratamiento de elección la extirpación quirúrgica, destacándose la cirugía micrográfica de Mohs por sus ventajas. Caso clínico: Se presenta un paciente masculino de 40 años, con un dermatofibrosarcoma protuberans en el dorso, a quien se le realizó exéresis mediante técnica de Mohs, sin recurrencia del tumor luego de dos años de seguimiento. Conclusión:  Es importante destacar que la técnica de Mohs presenta ventajas sobre la técnica convencional, permitiendo la optimización de tejidos, asegurando márgenes libres, y logrando una baja tasa de recidivas. Objetivo: O dermatofibrossarcoma protuberante é uma neoplasia sarcomatosa de baixa incidência. Apresenta um crescimento lento, no entanto, tem a capacidade de comprometer os tecidos profundos. Clinicamente, pode simular lesões benignas, apresentando-se como placas espessadas ou atróficas, que lentamente se transformam em lesões protuberantes. A excisão cirúrgica é proposta como tratamento de escolha, destacando-se a cirurgia micrográfica de Mohs por suas vantagens.  Caso clínico: Um paciente masculino de 40 anos apresentou dermatofibrossarcoma protuberante no dorso, submetido à excisão pela técnica de Mohs, sem recorrência do tumor após dois anos de acompanhamento. Conclusão: É importante destacar que a técnica de Mohs apresenta vantagens sobre a técnica convencional, permitindo a otimização de tecidos, garantindo margens livres e alcançando uma baixa taxa de recidiva. Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2025-03-31 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf text/html https://revistas.unc.edu.ar/index.php/med/article/view/45363 10.31053/1853.0605.v82.n1.45363 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 82 No. 1 (2025); 165-175 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 82 Núm. 1 (2025); 165-175 Revista da Faculdade de Ciências Médicas de Córdoba; v. 82 n. 1 (2025); 165-175 1853-0605 0014-6722 10.31053/1853.0605.v82.n1 spa https://revistas.unc.edu.ar/index.php/med/article/view/45363/48673 https://revistas.unc.edu.ar/index.php/med/article/view/45363/48634 Derechos de autor 2025 Universidad Nacional de Córdoba https://creativecommons.org/licenses/by-nc/4.0
institution Universidad Nacional de Córdoba
institution_str I-10
repository_str R-327
container_title_str Revista de la Facultad de Ciencias Médicas de Córdoba
language Español
format Artículo revista
topic dermatofibrosarcoma
mohs surgery
sarcoma
dermatofibrosarcoma
cirugía de mohs
sarcoma
dermatofibrossarcoma
cirurgia de mohs
sarcoma
spellingShingle dermatofibrosarcoma
mohs surgery
sarcoma
dermatofibrosarcoma
cirugía de mohs
sarcoma
dermatofibrossarcoma
cirurgia de mohs
sarcoma
Abeledo, Lía Salomé
Barbini, Carla
Russier, Gerardo
Busso, Corina
Barbini, Carla
Russier, Gerardo
Busso, Corina
Barbini, Carla
Russier, Gerardo
Busso, Corina
Dermatofibrosarcoma protuberans treated with Mohs surgery: case report
topic_facet dermatofibrosarcoma
mohs surgery
sarcoma
dermatofibrosarcoma
cirugía de mohs
sarcoma
dermatofibrossarcoma
cirurgia de mohs
sarcoma
author Abeledo, Lía Salomé
Barbini, Carla
Russier, Gerardo
Busso, Corina
Barbini, Carla
Russier, Gerardo
Busso, Corina
Barbini, Carla
Russier, Gerardo
Busso, Corina
author_facet Abeledo, Lía Salomé
Barbini, Carla
Russier, Gerardo
Busso, Corina
Barbini, Carla
Russier, Gerardo
Busso, Corina
Barbini, Carla
Russier, Gerardo
Busso, Corina
author_sort Abeledo, Lía Salomé
title Dermatofibrosarcoma protuberans treated with Mohs surgery: case report
title_short Dermatofibrosarcoma protuberans treated with Mohs surgery: case report
title_full Dermatofibrosarcoma protuberans treated with Mohs surgery: case report
title_fullStr Dermatofibrosarcoma protuberans treated with Mohs surgery: case report
title_full_unstemmed Dermatofibrosarcoma protuberans treated with Mohs surgery: case report
title_sort dermatofibrosarcoma protuberans treated with mohs surgery: case report
description Objectives: Dermatofibrosarcoma protuberans is a sarcomatous neoplasm with low incidence. It exhibits slow growth; however, it has the capacity to involve deep tissues. Clinically, it can mimic benign lesions, presenting as thickened or atrophic plaques that slowly transform into protruding lesions. The treatment of choice is surgical excision, with Mohs micrographic surgery standing out for its advantages. Clinical case: A 40-year-old male patient with dermatofibrosarcoma protuberans on the back underwent excision using the Mohs technique, with no tumor recurrence after two years of follow-up. Conclusion: It is important to highlight that the Mohs technique offers advantages over conventional methods, allowing for tissue optimization, ensuring clear margins, and achieving a low recurrence rate
publisher Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
publishDate 2025
url https://revistas.unc.edu.ar/index.php/med/article/view/45363
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first_indexed 2025-05-10T05:10:28Z
last_indexed 2025-05-10T05:10:28Z
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