Anatomy variant of the papillary muscles as a cause of mitral regurgitation. Case report of a parachute-like asymmetric mitral valve

Introduction: The parachute-like mitral valve is a congenital anomaly characterized by an asymmetric arrangement of the papillary muscles, with cardiac imaging being the procedure of choice both for anatomical diagnosis and for functional assessment of this type of structural anomaly. Clinical Ca...

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Autores principales: Briceño Revillo, Jorge Miguel, Ramon y Cajal Calvo, Juan, Melero Polo, Jorge, Cueva Recalde, Juan Francisco, Ibañez Muñoz, David
Formato: Artículo revista
Lenguaje:Español
Publicado: Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2021
Materias:
Acceso en línea:https://revistas.unc.edu.ar/index.php/med/article/view/33876
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institution Universidad Nacional de Córdoba
institution_str I-10
repository_str R-327
container_title_str Revista de la Facultad de Ciencias Médicas de Córdoba
language Español
format Artículo revista
topic mitral valve
papillary muscles
congenital abnormalities
válvula mitral
músculos papilares
anomalías congénitas
valva mitral
músculos papilares
anormalidades congénitas
spellingShingle mitral valve
papillary muscles
congenital abnormalities
válvula mitral
músculos papilares
anomalías congénitas
valva mitral
músculos papilares
anormalidades congénitas
Briceño Revillo, Jorge Miguel
Ramon y Cajal Calvo, Juan
Melero Polo, Jorge
Cueva Recalde, Juan Francisco
Ibañez Muñoz, David
Anatomy variant of the papillary muscles as a cause of mitral regurgitation. Case report of a parachute-like asymmetric mitral valve
topic_facet mitral valve
papillary muscles
congenital abnormalities
válvula mitral
músculos papilares
anomalías congénitas
valva mitral
músculos papilares
anormalidades congénitas
author Briceño Revillo, Jorge Miguel
Ramon y Cajal Calvo, Juan
Melero Polo, Jorge
Cueva Recalde, Juan Francisco
Ibañez Muñoz, David
author_facet Briceño Revillo, Jorge Miguel
Ramon y Cajal Calvo, Juan
Melero Polo, Jorge
Cueva Recalde, Juan Francisco
Ibañez Muñoz, David
author_sort Briceño Revillo, Jorge Miguel
title Anatomy variant of the papillary muscles as a cause of mitral regurgitation. Case report of a parachute-like asymmetric mitral valve
title_short Anatomy variant of the papillary muscles as a cause of mitral regurgitation. Case report of a parachute-like asymmetric mitral valve
title_full Anatomy variant of the papillary muscles as a cause of mitral regurgitation. Case report of a parachute-like asymmetric mitral valve
title_fullStr Anatomy variant of the papillary muscles as a cause of mitral regurgitation. Case report of a parachute-like asymmetric mitral valve
title_full_unstemmed Anatomy variant of the papillary muscles as a cause of mitral regurgitation. Case report of a parachute-like asymmetric mitral valve
title_sort anatomy variant of the papillary muscles as a cause of mitral regurgitation. case report of a parachute-like asymmetric mitral valve
description Introduction: The parachute-like mitral valve is a congenital anomaly characterized by an asymmetric arrangement of the papillary muscles, with cardiac imaging being the procedure of choice both for anatomical diagnosis and for functional assessment of this type of structural anomaly. Clinical Case: Patient with hemodynamic decompensation in which a parachute-like mitral valve disease was diagnosed incidentally. Image findings by transthoracic echocardiography and magnetic resonance revealed the presence of 2 papillary muscles, both with apical lateral segment insertion, confirming an asymmetric mitral valve similar to its parachute morphology. Discussion: The parachute mitral valve is an uncommon congenital anomaly constituting the presence of two papillary muscles, one of them being more elongated and adhering to the mitral leaflet in a contiguous way, showing in some cases small associated tendinous chords. It can present a benign evolution being a chance finding or associated with valvular hemodynamic repercussion as the case presented. Conclusion: The parachute-like mitral valve is a congenital anomaly characterized by an asymmetric arrangement of the papillary muscles, its evolution being highly variable, being able to go unnoticed or significantly affecting valve mechanics.
publisher Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
publishDate 2021
url https://revistas.unc.edu.ar/index.php/med/article/view/33876
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spelling I10-R327-article-338762021-12-29T20:14:46Z Anatomy variant of the papillary muscles as a cause of mitral regurgitation. Case report of a parachute-like asymmetric mitral valve Variante de la anatomía de los músculos papilares como causa de insuficiencia mitral. Un caso de válvula mitral asimétrica en paracaídas-like Variante da anatomia dos músculos papilares como causa da regurgitação mitral. Um caso de válvula mitral assimétrica semelhante a um pára-quedas Briceño Revillo, Jorge Miguel Ramon y Cajal Calvo, Juan Melero Polo, Jorge Cueva Recalde, Juan Francisco Ibañez Muñoz, David mitral valve papillary muscles congenital abnormalities válvula mitral músculos papilares anomalías congénitas valva mitral músculos papilares anormalidades congénitas Introduction: The parachute-like mitral valve is a congenital anomaly characterized by an asymmetric arrangement of the papillary muscles, with cardiac imaging being the procedure of choice both for anatomical diagnosis and for functional assessment of this type of structural anomaly. Clinical Case: Patient with hemodynamic decompensation in which a parachute-like mitral valve disease was diagnosed incidentally. Image findings by transthoracic echocardiography and magnetic resonance revealed the presence of 2 papillary muscles, both with apical lateral segment insertion, confirming an asymmetric mitral valve similar to its parachute morphology. Discussion: The parachute mitral valve is an uncommon congenital anomaly constituting the presence of two papillary muscles, one of them being more elongated and adhering to the mitral leaflet in a contiguous way, showing in some cases small associated tendinous chords. It can present a benign evolution being a chance finding or associated with valvular hemodynamic repercussion as the case presented. Conclusion: The parachute-like mitral valve is a congenital anomaly characterized by an asymmetric arrangement of the papillary muscles, its evolution being highly variable, being able to go unnoticed or significantly affecting valve mechanics. Introducción: La válvula mitral en paracaídas-like es una anomalía congénita caracterizada por una disposición asimétrica de los músculos papilares, siendo las pruebas de imagen cardiaca son el procedimiento de elección tanto para el diagnóstico anatómico como para realizar la valoración funcional de este tipo de anomalía estructural. Caso Clínico: Paciente con cuadro de descompensación hemodinámica en el cual se diagnóstica de manera incidental de una valvulopatía mitral en forma de paracaídas-like. Los hallazgos de imagen por ecocardiografía transtorácica y resonancia magnética ponen de manifiesto la presencia de 2 músculos papilares, ambos con inserción en segmento lateral apical confirmando una válvula mitral asimétrica con similitud a su morfología en paracaídas. Discusión: La válvula mitral en paracaídas es una anomalía congénita poco común constituyente en la presencia de dos músculos papilares siendo uno de ellos más elongado y adherido al velo mitral de forma contigua, mostrándose en algunos casos pequeñas cuerdas tendinosas asociadas. Puede presentar una evolución benigna siendo un hallazgo casual o asociarse a repercusión hemodinámica valvular como el caso presentado. Conclusión: La válvula mitral en paracaídas-like es una anomalía congénita caracterizada por una disposición asimétrica de los músculos papilares, siendo su evolución muy variable, pudiendo pasar desapercibida o afectando de forma significativa a la mecánica valvular. Introdução: A válvula mitral em forma de paraquedas é uma anomalia congênita caracterizada por um arranjo assimétrico dos músculos papilares, sendo a imagem cardíaca o procedimento de escolha tanto para diagnóstico anatômico quanto para avaliação funcional desse tipo de anomalia estrutural. Caso Clínico: Paciente com descompensação hemodinâmica com diagnóstico incidental de valvopatia mitral tipo pára-quedas. Os achados de imagem pela ecocardiografia transtorácica e ressonância magnética revelaram a presença de 2 músculos papilares, ambos com inserção do segmento lateral apical, confirmando uma válvula mitral assimétrica semelhante à sua morfologia de paraquedas. Discussão: A válvula mitral em pára-quedas é uma anomalia congênita incomum, constituindo-se na presença de dois músculos papilares, sendo um deles mais alongado e aderindo ao folheto mitral de forma contígua, apresentando em alguns casos pequenas cordas tendíneas associadas. Pode apresentar evolução benigna sendo achado casual ou associado a repercussão hemodinâmica valvar conforme o caso apresentado. Conclusão: A válvula mitral em forma de paraquedas é uma anomalia congênita caracterizada por um arranjo assimétrico dos músculos papilares, sendo sua evolução muito variável, podendo passar despercebida ou afetar significativamente a mecânica valvar. Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2021-12-28 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion text/html application/pdf https://revistas.unc.edu.ar/index.php/med/article/view/33876 10.31053/1853.0605.v78.n4.33876 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 78 No. 4 (2021); 402-404 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 78 Núm. 4 (2021); 402-404 Revista da Faculdade de Ciências Médicas de Córdoba; v. 78 n. 4 (2021); 402-404 1853-0605 0014-6722 10.31053/1853.0605.v78.n4 spa https://revistas.unc.edu.ar/index.php/med/article/view/33876/36432 https://revistas.unc.edu.ar/index.php/med/article/view/33876/36703 Derechos de autor 2021 Universidad Nacional de Córdoba http://creativecommons.org/licenses/by-nc/4.0