Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss): Case Report.
Eosinophilic granulomatosis with polyangiitis, formerly known as Churg-Strauss Syndrome, is a rare pathology that belongs to the group of diseases characterized by necrotizing vasculitis of small and medium-sized systemic blood vessels. Symptomatic cardiovascular involvement occurs in 27% to 47% of...
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Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2022
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| Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/32922 |
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I10-R327-article-329222022-08-19T21:47:05Z Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss): Case Report. Miocardiopatía dilatada en paciente con Granulomatosis Eosinofílica con Poliangeítis (Churg Strauss): Presentación de un caso. Miocardiopatia dilatada em paciente com granulomatose eosinofílica com poliangite. : Relato de um caso. Lozita, Julieta Vicentín, Judith Mailén Melgarejo Otarola, María Florencia Paolasso, Jorge Andrés Colque, Roberto Miguel Angel Sarmiento, Pablo Ezequiel cardiomyopathy, dilated churg-strauss syndrome heart failure cardiomiopatía dilatada síndrome de churg-strauss insuficiencia cardíaca cardiomiopatia dilatada síndrome de churg-strauss insuficiência cardíaca Eosinophilic granulomatosis with polyangiitis, formerly known as Churg-Strauss Syndrome, is a rare pathology that belongs to the group of diseases characterized by necrotizing vasculitis of small and medium-sized systemic blood vessels. Symptomatic cardiovascular involvement occurs in 27% to 47% of Churg-Strauss cases, being one of the most serious manifestations. The diagnosis is usually confirmed with tissue biopsy showing eosinophil infiltration, but with the recent inclusion of cardiac MRI, we can dispense with it. Early diagnosis is important because prompt treatment is usually associated with improvement in the condition. La granulomatosis eosinofílica con poliangeítis, anteriormente conocida como síndrome de Churg-Strauss, es una patología poco frecuente que pertenece al grupo de enfermedades caracterizadas por vasculitis necrotizante de vasos sanguíneos sistémicos de pequeño y mediano calibre. La afectación cardiovascular sintomática ocurre entre un 27% a un 47% de los casos de Churg-Strauss, siendo una de las manifestaciones más graves. El diagnóstico suele confirmarse con biopsia de tejido con infiltración de eosinófilos, pero con la reciente inclusión de la resonancia cardíaca, podemos prescindir de ella. El diagnóstico precoz es importante debido a que el tratamiento oportuno suele asociarse con mejoría del cuadro. A granulomatose eosinofílica com poliangiite é uma patologia pouco frequente que pertence ao grupo de enfermidade caracterizada por vasculite necrotizante dos vasos sanguíneos sistêmicos de pequeno e médio calibre. A afetação cardiovascular sintomática ocorre entre 27% a 47% dos casos de Churg Strauss, sendo uma das manifestações mais graves. O diagnóstico geralmente se confirma com biópsia de tecido mostrando a infiltração de eosinófilos, mas com a recente inclusão da ressonância cardíaca, podemos prescindir dela. O diagnóstico precoce é importante devido que o tratamento oportuno geralmente se associa com melhoria do quadro. Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2022-06-06 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf text/html https://revistas.unc.edu.ar/index.php/med/article/view/32922 10.31053/1853.0605.v79.n2.32922 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 79 No. 2 (2022); 193-196 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 79 Núm. 2 (2022); 193-196 Revista da Faculdade de Ciências Médicas de Córdoba; v. 79 n. 2 (2022); 193-196 1853-0605 0014-6722 10.31053/1853.0605.v79.n2 spa https://revistas.unc.edu.ar/index.php/med/article/view/32922/37938 https://revistas.unc.edu.ar/index.php/med/article/view/32922/37964 Derechos de autor 2022 Universidad Nacional de Córdoba http://creativecommons.org/licenses/by-nc/4.0 |
| institution |
Universidad Nacional de Córdoba |
| institution_str |
I-10 |
| repository_str |
R-327 |
| container_title_str |
Revista de la Facultad de Ciencias Médicas de Córdoba |
| language |
Español |
| format |
Artículo revista |
| topic |
cardiomyopathy, dilated churg-strauss syndrome heart failure cardiomiopatía dilatada síndrome de churg-strauss insuficiencia cardíaca cardiomiopatia dilatada síndrome de churg-strauss insuficiência cardíaca |
| spellingShingle |
cardiomyopathy, dilated churg-strauss syndrome heart failure cardiomiopatía dilatada síndrome de churg-strauss insuficiencia cardíaca cardiomiopatia dilatada síndrome de churg-strauss insuficiência cardíaca Lozita, Julieta Vicentín, Judith Mailén Melgarejo Otarola, María Florencia Paolasso, Jorge Andrés Colque, Roberto Miguel Angel Sarmiento, Pablo Ezequiel Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss): Case Report. |
| topic_facet |
cardiomyopathy, dilated churg-strauss syndrome heart failure cardiomiopatía dilatada síndrome de churg-strauss insuficiencia cardíaca cardiomiopatia dilatada síndrome de churg-strauss insuficiência cardíaca |
| author |
Lozita, Julieta Vicentín, Judith Mailén Melgarejo Otarola, María Florencia Paolasso, Jorge Andrés Colque, Roberto Miguel Angel Sarmiento, Pablo Ezequiel |
| author_facet |
Lozita, Julieta Vicentín, Judith Mailén Melgarejo Otarola, María Florencia Paolasso, Jorge Andrés Colque, Roberto Miguel Angel Sarmiento, Pablo Ezequiel |
| author_sort |
Lozita, Julieta |
| title |
Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss): Case Report. |
| title_short |
Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss): Case Report. |
| title_full |
Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss): Case Report. |
| title_fullStr |
Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss): Case Report. |
| title_full_unstemmed |
Dilated cardiomyopathy in a patient with Eosinophilic Granulomatosis with Polyangiitis (Churg Strauss): Case Report. |
| title_sort |
dilated cardiomyopathy in a patient with eosinophilic granulomatosis with polyangiitis (churg strauss): case report. |
| description |
Eosinophilic granulomatosis with polyangiitis, formerly known as Churg-Strauss Syndrome, is a rare pathology that belongs to the group of diseases characterized by necrotizing vasculitis of small and medium-sized systemic blood vessels. Symptomatic cardiovascular involvement occurs in 27% to 47% of Churg-Strauss cases, being one of the most serious manifestations. The diagnosis is usually confirmed with tissue biopsy showing eosinophil infiltration, but with the recent inclusion of cardiac MRI, we can dispense with it.
Early diagnosis is important because prompt treatment is usually associated with improvement in the condition. |
| publisher |
Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
| publishDate |
2022 |
| url |
https://revistas.unc.edu.ar/index.php/med/article/view/32922 |
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