Tomographic characteristics of solid-pseudopapillary neoplasms (Frantz tumor)
Introduction: Solid-pseudopapillary neoplasms (SPN), or Frantz tumor, is a rare, low-grade neoplasm that occurs mainly in young women. It was described in 1959 by Virginia Frantz and constitutes 0.2-2.7 % of all pancreatic tumors. Computed tomography (CT) plays an important role in the diagnosis of...
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Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2020
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Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/26228 |
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I10-R327-article-26228 |
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Universidad Nacional de Córdoba |
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I-10 |
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R-327 |
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Revista de la Facultad de Ciencias Médicas de Córdoba |
language |
Español |
format |
Artículo revista |
topic |
pancreatic neoplasms computed tomography Peru neoplasia pancreática tomografía Perú neoplasia pancreática tomografia Peru |
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pancreatic neoplasms computed tomography Peru neoplasia pancreática tomografía Perú neoplasia pancreática tomografia Peru Cerron-Vela, Carmen Rosa Moreno Navarro, Percy Araujo-Banchon, William J Tomographic characteristics of solid-pseudopapillary neoplasms (Frantz tumor) |
topic_facet |
pancreatic neoplasms computed tomography Peru neoplasia pancreática tomografía Perú neoplasia pancreática tomografia Peru |
author |
Cerron-Vela, Carmen Rosa Moreno Navarro, Percy Araujo-Banchon, William J |
author_facet |
Cerron-Vela, Carmen Rosa Moreno Navarro, Percy Araujo-Banchon, William J |
author_sort |
Cerron-Vela, Carmen Rosa |
title |
Tomographic characteristics of solid-pseudopapillary neoplasms (Frantz tumor) |
title_short |
Tomographic characteristics of solid-pseudopapillary neoplasms (Frantz tumor) |
title_full |
Tomographic characteristics of solid-pseudopapillary neoplasms (Frantz tumor) |
title_fullStr |
Tomographic characteristics of solid-pseudopapillary neoplasms (Frantz tumor) |
title_full_unstemmed |
Tomographic characteristics of solid-pseudopapillary neoplasms (Frantz tumor) |
title_sort |
tomographic characteristics of solid-pseudopapillary neoplasms (frantz tumor) |
description |
Introduction: Solid-pseudopapillary neoplasms (SPN), or Frantz tumor, is a rare, low-grade neoplasm that occurs mainly in young women. It was described in 1959 by Virginia Frantz and constitutes 0.2-2.7 % of all pancreatic tumors. Computed tomography (CT) plays an important role in the diagnosis of this pathology of scarce reporting. The objective of the present study is to describe the epidemiological and tomographic characteristics of the SPN in the Instituto Nacional de Enfermedades Neoplásicas (INEN) of Peru. Methods: Descriptive cross-sectional study performed with medical records of all patients diagnosed with SPN between 2004 and 2014. The variables described were tumor size, location, shape, borders, thickness of the capsule, composition, calcifications and uptake of contrast. The categorical variables were expressed in absolute and relative frequencies; while the numerical variables were described with median and interquartile deviation (ID). Statistical support STATA Version 12.0 was used. Results: Of all pancreatic cystic tumors (PCT), 51.9% corresponded to confirmed cases of TSP. The median age was 23.5 years. The isolated location in the head predominated (33.3%); the most frequent mixed location was body and tail (16.7%); diameter was more frequent between 5.1-10 cm and the content of the majority was predominantly solid. 30.0% of the NSP presented calcifications. Aim conclusion: Most cases of INP SPN (2004-2014) have similar characteristics to those reported in the international literature. |
publisher |
Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
publishDate |
2020 |
url |
https://revistas.unc.edu.ar/index.php/med/article/view/26228 |
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I10-R327-article-262282024-08-27T18:26:57Z Tomographic characteristics of solid-pseudopapillary neoplasms (Frantz tumor) Características tomográficas del tumor sólido pseudopapilar de páncreas (tumor de Frantz) Características tomográficas do tumor pseudopapilar de pâncreas sólido (tumor de Frantz) Cerron-Vela, Carmen Rosa Moreno Navarro, Percy Araujo-Banchon, William J pancreatic neoplasms computed tomography Peru neoplasia pancreática tomografía Perú neoplasia pancreática tomografia Peru Introduction: Solid-pseudopapillary neoplasms (SPN), or Frantz tumor, is a rare, low-grade neoplasm that occurs mainly in young women. It was described in 1959 by Virginia Frantz and constitutes 0.2-2.7 % of all pancreatic tumors. Computed tomography (CT) plays an important role in the diagnosis of this pathology of scarce reporting. The objective of the present study is to describe the epidemiological and tomographic characteristics of the SPN in the Instituto Nacional de Enfermedades Neoplásicas (INEN) of Peru. Methods: Descriptive cross-sectional study performed with medical records of all patients diagnosed with SPN between 2004 and 2014. The variables described were tumor size, location, shape, borders, thickness of the capsule, composition, calcifications and uptake of contrast. The categorical variables were expressed in absolute and relative frequencies; while the numerical variables were described with median and interquartile deviation (ID). Statistical support STATA Version 12.0 was used. Results: Of all pancreatic cystic tumors (PCT), 51.9% corresponded to confirmed cases of TSP. The median age was 23.5 years. The isolated location in the head predominated (33.3%); the most frequent mixed location was body and tail (16.7%); diameter was more frequent between 5.1-10 cm and the content of the majority was predominantly solid. 30.0% of the NSP presented calcifications. Aim conclusion: Most cases of INP SPN (2004-2014) have similar characteristics to those reported in the international literature. Introducción: El tumor sólido pseudopilar de páncreas (TSP), o tumor de Frantz, es una neoplasia rara de bajo grado que acontece principalmente en mujeres jóvenes. Fue descrita en 1959 por Virginia Frantz y constituye del 0.2-2.7% de todos los tumores pancreáticos. La tomografía computada (TC) desempeña un papel importante en el diagnóstico de esta patología de escaso reporte. El objetivo del presente estudio es describir las características epidemiológicas y tomográficas del TSP en el Instituto Nacional de Enfermedades Neoplásicas (INEN) del Perú. Métodos: Estudio transversal descriptivo realizado con historias clínicas (HC) de todos los pacientes con diagnóstico de TSP entre los años 2004 y 2014. Las variables descritas fueron tamaño del tumor, ubicación, forma, bordes, grosor de la cápsula, composición, calcificaciones y captación de contraste. Las variables categóricas fueron expresadas en frecuencias absolutas y relativas; mientras que las variables numéricas fueron descritas con mediana y desviación intercuartílica (DIC). Se utilizó como soporte estadístico STATA Versión 12.0. Resultados: De todos los tumores quísticos de páncreas (TQP), el 51.9 % correspondió a casos confirmados de TSP. La mediana de la edad fue 23.5 años. Predominó la ubicación aislada en cabeza (33.3 %); la ubicación mixta más frecuente fue la de cuerpo y cola (16.7 %); fue más frecuente el diámetro entre 5.1-10 cm y el contenido de la mayoría fue a predominio sólido. El 30.0 % de los TSP presentaron calcificaciones. Conclusión principal: La mayoría casos de TSP del INEN (2004-2014) tienen características similares a lo reportado en la literatura internacional. Introdução: O tumor sólido do pâncreas pseudopilar (TSP), ou tumor de Frantz, é uma neoplasia rara e de baixo grau que ocorre principalmente em mulheres jovens. Foi descrito em 1959 por Virginia Frantz e constitui 0,2-2,7% de todos os tumores pancreáticos. A tomografia computadorizada (TC) desempenha um papel importante no diagnóstico dessa patologia pouco relatada. O objetivo deste estudo é descrever as características epidemiológicas e tomográficas do TSP no Instituto Nacional de Enfermedades Neoplásicas (INEN) do Peru. Métodos: Estudo descritivo transversal, realizado com histórico clínico (HC) de todos os pacientes diagnosticados com TSP entre 2004 e 2014. As variáveis descritas foram tamanho do tumor, localização, forma, bordas, espessura da cápsula, composição, calcificações e captação de contraste. As variáveis categóricas foram expressas em frequências absolutas e relativas; enquanto as variáveis numéricas foram descritas com mediana e desvio interquartil. Foi utilizado como suporte estatístico STATA Versão 12.0. Resultados: De todos os tumores do pâncreas cístico, 51,9% corresponderam a casos confirmados de TSP. A idade média foi de 23,5 anos. A localização isolada da cabeça predominou (33,3%); a localização mista mais frequente foi a do corpo e cauda (16,7%); o diâmetro entre 5,1-10 cm foi mais frequente e o conteúdo da maioria foi predominantemente sólido. 30,0% dos TSP apresentaram calcificações. Conclusão principal: A maioria dos casos de TSP do INEN (2004-2014) possui características semelhantes às relatadas na literatura internacional. Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2020-03-16 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf text/html https://revistas.unc.edu.ar/index.php/med/article/view/26228 10.31053/1853.0605.v77.n1.26228 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 77 No. 1 (2020); 33-38 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 77 Núm. 1 (2020); 33-38 Revista da Faculdade de Ciências Médicas de Córdoba; v. 77 n. 1 (2020); 33-38 1853-0605 0014-6722 10.31053/1853.0605.v77.n1 spa https://revistas.unc.edu.ar/index.php/med/article/view/26228/29404 https://revistas.unc.edu.ar/index.php/med/article/view/26228/29405 Derechos de autor 2020 Universidad Nacional de Córdoba https://creativecommons.org/licenses/by-nc/4.0 |