Insipid diabetes as initial presentation of Wegener´s granulomatosis

Wegener´s granulomatosis is a granulomatous necrotizing vasculitis which predominantly affects the respiratory tract, kidney, and less frequently other organs such as the nervous system. The latter may occur in up to 54% of cases and when it does it is more frequently of the peripheral nerves. We pr...

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Autores principales: Ponce, Lorena Narváez, Carrió, Judith, Soriano, Enrique R., Santos, Carlos D., Imamura, Patricia M., Catoggio, Luis J.
Formato: Artículo revista
Lenguaje:Español
Publicado: Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2009
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Acceso en línea:https://revistas.unc.edu.ar/index.php/med/article/view/23538
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spelling I10-R327-article-235382024-08-27T18:24:33Z Insipid diabetes as initial presentation of Wegener´s granulomatosis Diabetes Insípida como forma de presentación de Granulomatosis de Wegener Ponce, Lorena Narváez Carrió, Judith Soriano, Enrique R. Santos, Carlos D. Imamura, Patricia M. Catoggio, Luis J. Granulomatosis de Wegener diabetes insípida compromiso neurologico Wegener´s granulomatosis insipid diabetes neurologic involvement Wegener´s granulomatosis is a granulomatous necrotizing vasculitis which predominantly affects the respiratory tract, kidney, and less frequently other organs such as the nervous system. The latter may occur in up to 54% of cases and when it does it is more frequently of the peripheral nerves. We present a 19 year old woman who commenced her disease with involvement of respiratory sinuses, lungs and kidney and who developed central insipid diabetes (CID) at onset. The CID persisted in spite of adequate response of the other organs and systems with immunosuppresor treatment. The development of CID in the context of vasculitis should suggest this as a possible mechanism. La Granulomatosis de Wegener es una vasculitis granulomatosa necrotizante que afecta preferentemente al aparato respiratorio, riñón y menos frecuentemente a otros sistemas como el nervioso. Esto último ocurre hasta en el 54 % de los casos, siendo mas frecuente el compromiso del sistema nervioso periférico.Presentamos el caso de una mujer de 19 años que debuta con compromiso de senos paranasales, pulmón, riñón y que desarrolla además, de inicio, diabetes insípida central ( D.I.C ). Este cuadro persiste aún luego de recibir tratamiento inmunosupresor que logra revertir el compromiso de los otros sistemas. La Aparición de un cuadro de DIC en el contexto de una vasculitis debe sugerir a ésta como posible mecanismo causal. Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2009-02-25 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf https://revistas.unc.edu.ar/index.php/med/article/view/23538 10.31053/1853.0605.v66.n1.23538 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 66 No. 1 (2009); 31-35 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 66 Núm. 1 (2009); 31-35 Revista da Faculdade de Ciências Médicas de Córdoba; v. 66 n. 1 (2009); 31-35 1853-0605 0014-6722 10.31053/1853.0605.v66.n1 spa https://revistas.unc.edu.ar/index.php/med/article/view/23538/23242 Derechos de autor 2009 Universidad Nacional de Córdoba https://creativecommons.org/licenses/by-nc/4.0
institution Universidad Nacional de Córdoba
institution_str I-10
repository_str R-327
container_title_str Revista de la Facultad de Ciencias Médicas de Córdoba
language Español
format Artículo revista
topic Granulomatosis de Wegener
diabetes insípida
compromiso neurologico
Wegener´s granulomatosis
insipid diabetes
neurologic involvement
spellingShingle Granulomatosis de Wegener
diabetes insípida
compromiso neurologico
Wegener´s granulomatosis
insipid diabetes
neurologic involvement
Ponce, Lorena Narváez
Carrió, Judith
Soriano, Enrique R.
Santos, Carlos D.
Imamura, Patricia M.
Catoggio, Luis J.
Insipid diabetes as initial presentation of Wegener´s granulomatosis
topic_facet Granulomatosis de Wegener
diabetes insípida
compromiso neurologico
Wegener´s granulomatosis
insipid diabetes
neurologic involvement
author Ponce, Lorena Narváez
Carrió, Judith
Soriano, Enrique R.
Santos, Carlos D.
Imamura, Patricia M.
Catoggio, Luis J.
author_facet Ponce, Lorena Narváez
Carrió, Judith
Soriano, Enrique R.
Santos, Carlos D.
Imamura, Patricia M.
Catoggio, Luis J.
author_sort Ponce, Lorena Narváez
title Insipid diabetes as initial presentation of Wegener´s granulomatosis
title_short Insipid diabetes as initial presentation of Wegener´s granulomatosis
title_full Insipid diabetes as initial presentation of Wegener´s granulomatosis
title_fullStr Insipid diabetes as initial presentation of Wegener´s granulomatosis
title_full_unstemmed Insipid diabetes as initial presentation of Wegener´s granulomatosis
title_sort insipid diabetes as initial presentation of wegener´s granulomatosis
description Wegener´s granulomatosis is a granulomatous necrotizing vasculitis which predominantly affects the respiratory tract, kidney, and less frequently other organs such as the nervous system. The latter may occur in up to 54% of cases and when it does it is more frequently of the peripheral nerves. We present a 19 year old woman who commenced her disease with involvement of respiratory sinuses, lungs and kidney and who developed central insipid diabetes (CID) at onset. The CID persisted in spite of adequate response of the other organs and systems with immunosuppresor treatment. The development of CID in the context of vasculitis should suggest this as a possible mechanism.
publisher Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
publishDate 2009
url https://revistas.unc.edu.ar/index.php/med/article/view/23538
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