Pulmonary restriction secondary to cutaneous sclerosis caused by chronic graft versus host disease: Case Report
Chronic graft versus host disease (GVHD) is a major complication of the allogeneic stem cell transplant. One of most frequent manifestations of GVHD is the cutaneous compromise with the sclerodermatous variety being the most severe. We considered that the restrictive respiratory compromise and its e...
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| Autores principales: | , , , |
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| Formato: | Artículo revista |
| Lenguaje: | Español |
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Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2019
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| Materias: | |
| Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/21090 |
| Aporte de: |
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I10-R327-article-21090 |
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ojs |
| institution |
Universidad Nacional de Córdoba |
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I-10 |
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R-327 |
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Revista de la Facultad de Ciencias Médicas de Córdoba |
| language |
Español |
| format |
Artículo revista |
| topic |
enfermedades pulmonares enfermedad injerto contra huésped trasplante de medula ósea pruebas de función respiratoria lung diseases graft-versus-host disease bone marrow transplantation respiratory function tests. pneumopatias doença enxerto-hospedeiro transplante de medula óssea y testes de função pilmonar |
| spellingShingle |
enfermedades pulmonares enfermedad injerto contra huésped trasplante de medula ósea pruebas de función respiratoria lung diseases graft-versus-host disease bone marrow transplantation respiratory function tests. pneumopatias doença enxerto-hospedeiro transplante de medula óssea y testes de função pilmonar Castro, Horacio Matias Castro Azcurra, Rodrigo Sebastián Basquiera, Ana Lisa De Vito, Eduardo Luis Pulmonary restriction secondary to cutaneous sclerosis caused by chronic graft versus host disease: Case Report |
| topic_facet |
enfermedades pulmonares enfermedad injerto contra huésped trasplante de medula ósea pruebas de función respiratoria lung diseases graft-versus-host disease bone marrow transplantation respiratory function tests. pneumopatias doença enxerto-hospedeiro transplante de medula óssea y testes de função pilmonar |
| author |
Castro, Horacio Matias Castro Azcurra, Rodrigo Sebastián Basquiera, Ana Lisa De Vito, Eduardo Luis |
| author_facet |
Castro, Horacio Matias Castro Azcurra, Rodrigo Sebastián Basquiera, Ana Lisa De Vito, Eduardo Luis |
| author_sort |
Castro, Horacio Matias |
| title |
Pulmonary restriction secondary to cutaneous sclerosis caused by chronic graft versus host disease: Case Report |
| title_short |
Pulmonary restriction secondary to cutaneous sclerosis caused by chronic graft versus host disease: Case Report |
| title_full |
Pulmonary restriction secondary to cutaneous sclerosis caused by chronic graft versus host disease: Case Report |
| title_fullStr |
Pulmonary restriction secondary to cutaneous sclerosis caused by chronic graft versus host disease: Case Report |
| title_full_unstemmed |
Pulmonary restriction secondary to cutaneous sclerosis caused by chronic graft versus host disease: Case Report |
| title_sort |
pulmonary restriction secondary to cutaneous sclerosis caused by chronic graft versus host disease: case report |
| description |
Chronic graft versus host disease (GVHD) is a major complication of the allogeneic stem cell transplant. One of most frequent manifestations of GVHD is the cutaneous compromise with the sclerodermatous variety being the most severe. We considered that the restrictive respiratory compromise and its evolution are not well characterized. We described the functional respiratory alterations of a patient with sclerodermatous chronic GVHD and considered differential diagnosis of pulmonary restriction in this type of patient. We reported the case of a 21-year-old woman with pulmonary restriction secondary to cutaneous sclerosis which was caused by chronic GVHD. This report illustrates the importance of utilizing both functional respiratory tests and diagnosis images to accurately characterize the cause of the respiratory compromise. We believe that the functional alterations described in this case could be caused by the cutaneous disorder found. |
| publisher |
Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
| publishDate |
2019 |
| url |
https://revistas.unc.edu.ar/index.php/med/article/view/21090 |
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I10-R327-article-210902024-08-27T18:22:37Z Pulmonary restriction secondary to cutaneous sclerosis caused by chronic graft versus host disease: Case Report Restricción pulmonar secundaria a esclerosis cutánea por enfermedad injerto contra huésped crónica: Reporte de Caso Restrição pulmonar secundária à esclerose cutânea por doença do enxerto contra o hospedeiro: relato de caso. Castro, Horacio Matias Castro Azcurra, Rodrigo Sebastián Basquiera, Ana Lisa De Vito, Eduardo Luis enfermedades pulmonares enfermedad injerto contra huésped trasplante de medula ósea pruebas de función respiratoria lung diseases graft-versus-host disease bone marrow transplantation respiratory function tests. pneumopatias doença enxerto-hospedeiro transplante de medula óssea y testes de função pilmonar Chronic graft versus host disease (GVHD) is a major complication of the allogeneic stem cell transplant. One of most frequent manifestations of GVHD is the cutaneous compromise with the sclerodermatous variety being the most severe. We considered that the restrictive respiratory compromise and its evolution are not well characterized. We described the functional respiratory alterations of a patient with sclerodermatous chronic GVHD and considered differential diagnosis of pulmonary restriction in this type of patient. We reported the case of a 21-year-old woman with pulmonary restriction secondary to cutaneous sclerosis which was caused by chronic GVHD. This report illustrates the importance of utilizing both functional respiratory tests and diagnosis images to accurately characterize the cause of the respiratory compromise. We believe that the functional alterations described in this case could be caused by the cutaneous disorder found. La enfermedad injerto contra huésped crónica (EICH) es una complicación mayor del trasplante de células progenitoras alogénico. Una de sus manifestaciones más frecuentes es el compromiso cutáneo, siendo su variedad esclerodermiforme la más severa. El compromiso respiratorio, predominantemente restrictivo y su evolución no han sido bien caracterizados. El caso describe las alteraciones funcionales respiratorias de una paciente con EICH cutánea crónica tipo esclerodermiforme en dos momentos de su evolución y considera los diagnósticos diferenciales que producen restricción en estos pacientes. Se presenta el caso de una mujer de 21 años con restricción pulmonar secundaria a esclerosis cutánea por EICH. Este caso ilustra la relevancia de la utilización conjunta de las pruebas funcionales respiratorias y de los métodos diagnósticos por imágenes para caracterizar adecuadamente el compromiso respiratorio de estos pacientes. A nuestro juicio las alteraciones funcionales respiratorias descriptas pueden ser explicadas por el trastorno cutáneo hallado. A doença do enxerto contra o hospedeiro (DECH) é uma complicação importante do transplante halogênico de células hematopoéticas. Uma de suas manifestações mais frequentes é o envolvimento cutâneo, sendo sua variedade esclerodermia a mais grave. Compromisso respiratório, predominantemente restritivo e sua evolução não tem sido bem caracterizada. O caso descreve as alterações funcionais respiratórias de uma paciente com DECH tipo esclerodermia cutânea crônica em dois pontos de sua evolução e considera os diagnósticos diferenciais que produzem restrição nesses pacientes. Apresentamos o caso de uma mulher de 21 anos com restrição pulmonar secundária a esclerose cutânea por DECH. Este caso ilustra a relevância da utilização combinada de testes de funcão pulmonar e métodos de diagnóstico por imagem para caracterizar adequadamente o comprometimento respiratório desses pacientes. Em nossa opinião, as alterações funcionais respiratórias descritas podem ser explicadas por distúrbio cutâneo encontrado. Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2019-08-29 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf text/html application/vnd.openxmlformats-officedocument.spreadsheetml.sheet image/tiff image/tiff image/tiff https://revistas.unc.edu.ar/index.php/med/article/view/21090 10.31053/1853.0605.v76.n3.21090 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 76 No. 3 (2019); 189-192 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 76 Núm. 3 (2019); 189-192 Revista da Faculdade de Ciências Médicas de Córdoba; v. 76 n. 3 (2019); 189-192 1853-0605 0014-6722 10.31053/1853.0605.v76.n3 spa https://revistas.unc.edu.ar/index.php/med/article/view/21090/24485 https://revistas.unc.edu.ar/index.php/med/article/view/21090/24566 https://revistas.unc.edu.ar/index.php/med/article/view/21090/27005 https://revistas.unc.edu.ar/index.php/med/article/view/21090/27006 https://revistas.unc.edu.ar/index.php/med/article/view/21090/27007 https://revistas.unc.edu.ar/index.php/med/article/view/21090/27008 Derechos de autor 2019 Universidad Nacional de Córdoba https://creativecommons.org/licenses/by-nc/4.0 |