Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report

IntroductionIdiopathic systemic capillary leak syndrome (ISCLS) or Clarkson's disease is unusual but potentially lethal, characterized by recurrent shock incidents and anasarca secondary to idiopathic increase of capillary permeability. In such a context, the use of venoarterial Extracorporeal...

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Autores principales: Ortega, Florencia, Carboni Bisso, Indalecio, Fernandez Ceballos, Ignacio, Montserrat Rivera, Ana, Tisminetzky, Manuel, Dianti, José, San Román, Eduardo, Villarroel, Sonia, Di Stefano, Sabrina, Las Heras, Marcos
Formato: Artículo revista
Lenguaje:Español
Publicado: Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2020
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Acceso en línea:https://revistas.unc.edu.ar/index.php/med/article/view/26960
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id I10-R10article-26960
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institution Universidad Nacional de Córdoba
institution_str I-10
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container_title_str Revistas de la UNC
language Español
format Artículo revista
topic capillary leak syndrome
Clarkson disease
extracorporeal membrane oxygenation
critical care
síndrome de fuga capilar
oxigenación por membrana extracorpórea
cuidados críticos
síndrome de vazamento capilar
oxigenação por membrana extracorpórea
cuidados críticos
spellingShingle capillary leak syndrome
Clarkson disease
extracorporeal membrane oxygenation
critical care
síndrome de fuga capilar
oxigenación por membrana extracorpórea
cuidados críticos
síndrome de vazamento capilar
oxigenação por membrana extracorpórea
cuidados críticos
Ortega, Florencia
Carboni Bisso, Indalecio
Fernandez Ceballos, Ignacio
Montserrat Rivera, Ana
Tisminetzky, Manuel
Dianti, José
San Román, Eduardo
Villarroel, Sonia
Di Stefano, Sabrina
Las Heras, Marcos
Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report
topic_facet capillary leak syndrome
Clarkson disease
extracorporeal membrane oxygenation
critical care
síndrome de fuga capilar
oxigenación por membrana extracorpórea
cuidados críticos
síndrome de vazamento capilar
oxigenação por membrana extracorpórea
cuidados críticos
author Ortega, Florencia
Carboni Bisso, Indalecio
Fernandez Ceballos, Ignacio
Montserrat Rivera, Ana
Tisminetzky, Manuel
Dianti, José
San Román, Eduardo
Villarroel, Sonia
Di Stefano, Sabrina
Las Heras, Marcos
author_facet Ortega, Florencia
Carboni Bisso, Indalecio
Fernandez Ceballos, Ignacio
Montserrat Rivera, Ana
Tisminetzky, Manuel
Dianti, José
San Román, Eduardo
Villarroel, Sonia
Di Stefano, Sabrina
Las Heras, Marcos
author_sort Ortega, Florencia
title Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report
title_short Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report
title_full Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report
title_fullStr Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report
title_full_unstemmed Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report
title_sort use of extracorporeal membrane oxygenation in idiopathic capillary leak syndrome: a case report
description IntroductionIdiopathic systemic capillary leak syndrome (ISCLS) or Clarkson's disease is unusual but potentially lethal, characterized by recurrent shock incidents and anasarca secondary to idiopathic increase of capillary permeability. In such a context, the use of venoarterial Extracorporeal Membrane Oxygenation (ECMO) as cardiorespiratory support is a rescue action that seeks hemodynamic stability generation until spontaneous disappearance of the capillary occurs with the objective of surpassing the complications of resorption phase.  Case ReportA 42 year old patient presented ISCLS and required ECMO as hemodynamic support for 8 days. She remained 20 days in Intensive Care Unit and was given hospital release after 43 days. ConclusionsThe use of ECMO in the reported case was a useful strategy in the ISCLS management as a bridge to recovery both in the leak stage and the fluid resorption phase. Notwithstanding its indication is limited to thoroughly selected patients and requires further debate between specialists about its risks and benefits. 
publisher Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
publishDate 2020
url https://revistas.unc.edu.ar/index.php/med/article/view/26960
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