Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report
IntroductionIdiopathic systemic capillary leak syndrome (ISCLS) or Clarkson's disease is unusual but potentially lethal, characterized by recurrent shock incidents and anasarca secondary to idiopathic increase of capillary permeability. In such a context, the use of venoarterial Extracorporeal...
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Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2020
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Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/26960 |
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I10-R10article-26960 |
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Universidad Nacional de Córdoba |
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Revistas de la UNC |
language |
Español |
format |
Artículo revista |
topic |
capillary leak syndrome Clarkson disease extracorporeal membrane oxygenation critical care síndrome de fuga capilar oxigenación por membrana extracorpórea cuidados críticos síndrome de vazamento capilar oxigenação por membrana extracorpórea cuidados críticos |
spellingShingle |
capillary leak syndrome Clarkson disease extracorporeal membrane oxygenation critical care síndrome de fuga capilar oxigenación por membrana extracorpórea cuidados críticos síndrome de vazamento capilar oxigenação por membrana extracorpórea cuidados críticos Ortega, Florencia Carboni Bisso, Indalecio Fernandez Ceballos, Ignacio Montserrat Rivera, Ana Tisminetzky, Manuel Dianti, José San Román, Eduardo Villarroel, Sonia Di Stefano, Sabrina Las Heras, Marcos Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report |
topic_facet |
capillary leak syndrome Clarkson disease extracorporeal membrane oxygenation critical care síndrome de fuga capilar oxigenación por membrana extracorpórea cuidados críticos síndrome de vazamento capilar oxigenação por membrana extracorpórea cuidados críticos |
author |
Ortega, Florencia Carboni Bisso, Indalecio Fernandez Ceballos, Ignacio Montserrat Rivera, Ana Tisminetzky, Manuel Dianti, José San Román, Eduardo Villarroel, Sonia Di Stefano, Sabrina Las Heras, Marcos |
author_facet |
Ortega, Florencia Carboni Bisso, Indalecio Fernandez Ceballos, Ignacio Montserrat Rivera, Ana Tisminetzky, Manuel Dianti, José San Román, Eduardo Villarroel, Sonia Di Stefano, Sabrina Las Heras, Marcos |
author_sort |
Ortega, Florencia |
title |
Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report |
title_short |
Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report |
title_full |
Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report |
title_fullStr |
Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report |
title_full_unstemmed |
Use of Extracorporeal Membrane Oxygenation in idiopathic capillary leak syndrome: a case report |
title_sort |
use of extracorporeal membrane oxygenation in idiopathic capillary leak syndrome: a case report |
description |
IntroductionIdiopathic systemic capillary leak syndrome (ISCLS) or Clarkson's disease is unusual but potentially lethal, characterized by recurrent shock incidents and anasarca secondary to idiopathic increase of capillary permeability. In such a context, the use of venoarterial Extracorporeal Membrane Oxygenation (ECMO) as cardiorespiratory support is a rescue action that seeks hemodynamic stability generation until spontaneous disappearance of the capillary occurs with the objective of surpassing the complications of resorption phase.
Case ReportA 42 year old patient presented ISCLS and required ECMO as hemodynamic support for 8 days. She remained 20 days in Intensive Care Unit and was given hospital release after 43 days.
ConclusionsThe use of ECMO in the reported case was a useful strategy in the ISCLS management as a bridge to recovery both in the leak stage and the fluid resorption phase. Notwithstanding its indication is limited to thoroughly selected patients and requires further debate between specialists about its risks and benefits. |
publisher |
Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
publishDate |
2020 |
url |
https://revistas.unc.edu.ar/index.php/med/article/view/26960 |
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