Bronchopulmonary sarcoidosis. Brief review and description de 8 cases
Sarcoidosis is a disease of unknown etiology aífecting most frequently young adults. Diagnosis is based on clinical, radiological and histopathological features and presentation is frequently of constitutional and respiratory symptoms, hilar and mediastinal adenopathies...
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Formato: | Artículo revista |
Lenguaje: | Español |
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Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2019
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Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/26425 |
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Universidad Nacional de Córdoba |
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Revistas de la UNC |
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Español |
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Artículo revista |
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spellingShingle |
. Cambursano, H Casaux, A Langer, M Paramio, L Sarquis, G Zaya, A Sambuelli, R Bronchopulmonary sarcoidosis. Brief review and description de 8 cases |
topic_facet |
. |
author |
Cambursano, H Casaux, A Langer, M Paramio, L Sarquis, G Zaya, A Sambuelli, R |
author_facet |
Cambursano, H Casaux, A Langer, M Paramio, L Sarquis, G Zaya, A Sambuelli, R |
author_sort |
Cambursano, H |
title |
Bronchopulmonary sarcoidosis. Brief review and description de 8 cases |
title_short |
Bronchopulmonary sarcoidosis. Brief review and description de 8 cases |
title_full |
Bronchopulmonary sarcoidosis. Brief review and description de 8 cases |
title_fullStr |
Bronchopulmonary sarcoidosis. Brief review and description de 8 cases |
title_full_unstemmed |
Bronchopulmonary sarcoidosis. Brief review and description de 8 cases |
title_sort |
bronchopulmonary sarcoidosis. brief review and description de 8 cases |
description |
Sarcoidosis is a disease of unknown etiology aífecting most frequently young adults. Diagnosis is based on clinical, radiological and histopathological features and presentation is frequently of constitutional and respiratory symptoms, hilar and mediastinal adenopathies, with or without parenquimal involvement. Confirmation is histopathological with demonstration of non-caseificating granulomas in affected organs, with negative cultures for mycobacteria and fungi. We describe the clínica], radiological and istopathological findings in 8 patients. Mean age was 44 years (28-59) and haif the patients were maje. 'T\vo patients were symptom-free at diagnosis, thoracic findings were present in five (cough, retroesternal pain and arrhythmias) and one had extrathoracic symptoms (ankle arthritis). All showed mediastinal adenopathies In radiological and tomographic images (six were in stage 2 and Iwo in stage 1). TWo patients had spontaneous remission, four received oral sterolds, one required oral sterolds and azathioprine and there was no treatment data on one patient. In one patient, recidiva of severe and bilateral erithema nodosum required long terrn treatment with steroids and immunosupressors. Although sarcoidosis is a low revalent disease in our country, a hlgh index of suspicion is advisable when facing patients with respiratory symptoms, parenquimal involvement and mediastinal adenopathies, with or without extrathoracic manifestatlons. |
publisher |
Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
publishDate |
2019 |
url |
https://revistas.unc.edu.ar/index.php/med/article/view/26425 |
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Revistas |
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