Appendiceal collision tumor: Mucinous epithelial neoplasm and neuroendocrine tumor
Introduction: An appendiceal collision tumor is defined as the presence of histologically distinct types of tumors in the appendix without transition between them. Appendiceal tumors are rare, with epithelial neoplasms and neuroendocrine tumors being the most common. Objective: Report the case of wo...
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Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2020
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Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/25071 |
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I10-R10-article-25071 |
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Universidad Nacional de Córdoba |
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Revistas de la UNC |
language |
Español |
format |
Artículo revista |
topic |
appendiceal neoplasm neuroendocrine tumors carcinoid tumor cystadenoma mucinous neoplasias del apéndice tumores neuroendocrinos tumor carcinoide cistoadenoma mucinoso neoplasias do apêndice tumores neuroendócrine tumor carcinoide cistadenoma mucinoso |
spellingShingle |
appendiceal neoplasm neuroendocrine tumors carcinoid tumor cystadenoma mucinous neoplasias del apéndice tumores neuroendocrinos tumor carcinoide cistoadenoma mucinoso neoplasias do apêndice tumores neuroendócrine tumor carcinoide cistadenoma mucinoso Cafaro, Mario Alberto Yaryura Montero, José Gabriel Bianco, Agustín Petersen, María Laura Cárdenas Villa, Roberto Darío Cardozo Dutra, Blanca Badra, Roberto Miguel Appendiceal collision tumor: Mucinous epithelial neoplasm and neuroendocrine tumor |
topic_facet |
appendiceal neoplasm neuroendocrine tumors carcinoid tumor cystadenoma mucinous neoplasias del apéndice tumores neuroendocrinos tumor carcinoide cistoadenoma mucinoso neoplasias do apêndice tumores neuroendócrine tumor carcinoide cistadenoma mucinoso |
author |
Cafaro, Mario Alberto Yaryura Montero, José Gabriel Bianco, Agustín Petersen, María Laura Cárdenas Villa, Roberto Darío Cardozo Dutra, Blanca Badra, Roberto Miguel |
author_facet |
Cafaro, Mario Alberto Yaryura Montero, José Gabriel Bianco, Agustín Petersen, María Laura Cárdenas Villa, Roberto Darío Cardozo Dutra, Blanca Badra, Roberto Miguel |
author_sort |
Cafaro, Mario Alberto |
title |
Appendiceal collision tumor: Mucinous epithelial neoplasm and neuroendocrine tumor |
title_short |
Appendiceal collision tumor: Mucinous epithelial neoplasm and neuroendocrine tumor |
title_full |
Appendiceal collision tumor: Mucinous epithelial neoplasm and neuroendocrine tumor |
title_fullStr |
Appendiceal collision tumor: Mucinous epithelial neoplasm and neuroendocrine tumor |
title_full_unstemmed |
Appendiceal collision tumor: Mucinous epithelial neoplasm and neuroendocrine tumor |
title_sort |
appendiceal collision tumor: mucinous epithelial neoplasm and neuroendocrine tumor |
description |
Introduction: An appendiceal collision tumor is defined as the presence of histologically distinct types of tumors in the appendix without transition between them. Appendiceal tumors are rare, with epithelial neoplasms and neuroendocrine tumors being the most common. Objective: Report the case of woman with acute appendicitis and diagnosis of an appendiceal collision tumor. Case presentation: A 35 years old woman, who consulted for a 24 hours of continuous epigastric pain with migration to the right iliac fossa; the routine blood test showed leukocytosis with neutrophilia and an ultrasound scan abdomen demonstratedsigns in favor of acute appendicitis; a diagnosis of acute appendicitis and surgical treatment. The anatomopathological study and immunostaining revealed well-differentiated neuroendocrine neoplasia and low-grade mucinous epithelial neoplasia. A follow-up with postsurgical tumor markers was performed with normal results, in addition to computed tomography and postoperative colonoscopy without alterations. Discussion: Appendiceal collision tumor is infrequently. Generally the diagnosis is made with anatomopathological study and supposes great challenges for postoperative control because there are no guidelines to follow up. Conclusion: More research should be done in order to have recommendations for this disease. |
publisher |
Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
publishDate |
2020 |
url |
https://revistas.unc.edu.ar/index.php/med/article/view/25071 |
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I10-R10-article-250712020-06-19T15:10:10Z Appendiceal collision tumor: Mucinous epithelial neoplasm and neuroendocrine tumor Tumor de colisión apendicular: Neoplasia epitelial mucinosa y tumor neuroendocrino Tumor de colisão apendicular: Neoplasia epitelial mucinosa e tumor neuroendócrino Cafaro, Mario Alberto Yaryura Montero, José Gabriel Bianco, Agustín Petersen, María Laura Cárdenas Villa, Roberto Darío Cardozo Dutra, Blanca Badra, Roberto Miguel appendiceal neoplasm neuroendocrine tumors carcinoid tumor cystadenoma mucinous neoplasias del apéndice tumores neuroendocrinos tumor carcinoide cistoadenoma mucinoso neoplasias do apêndice tumores neuroendócrine tumor carcinoide cistadenoma mucinoso Introduction: An appendiceal collision tumor is defined as the presence of histologically distinct types of tumors in the appendix without transition between them. Appendiceal tumors are rare, with epithelial neoplasms and neuroendocrine tumors being the most common. Objective: Report the case of woman with acute appendicitis and diagnosis of an appendiceal collision tumor. Case presentation: A 35 years old woman, who consulted for a 24 hours of continuous epigastric pain with migration to the right iliac fossa; the routine blood test showed leukocytosis with neutrophilia and an ultrasound scan abdomen demonstratedsigns in favor of acute appendicitis; a diagnosis of acute appendicitis and surgical treatment. The anatomopathological study and immunostaining revealed well-differentiated neuroendocrine neoplasia and low-grade mucinous epithelial neoplasia. A follow-up with postsurgical tumor markers was performed with normal results, in addition to computed tomography and postoperative colonoscopy without alterations. Discussion: Appendiceal collision tumor is infrequently. Generally the diagnosis is made with anatomopathological study and supposes great challenges for postoperative control because there are no guidelines to follow up. Conclusion: More research should be done in order to have recommendations for this disease. Introducción: Se define a un tumor de colisión apendicular, como la presencia de dos tipos de tumores histológicamente distintos, dentro del apéndice sin transición entre ellos. Los tumores apendiculares son poco frecuentes, siendo las neoplasias epiteliales y los tumores neuroendocrinos los más comunes. Objetivo: Presentar el caso de una paciente con diagnóstico de tumor de colisión apendicular que se presentó como apendicitis aguda. Caso clínico: Mujer de 35 años de edad sin antecedentes patológicos que consultó por dolor epigástrico de 24 horas de evolución, con migración a fosa ilíaca derecha, de tipo continuo. El examen físico reveló un abdomen blando con defensa en fosa ilíaca derecha; el análisis de sangre mostró leucocitosis con neutrofilia y una ecografía en favor de apendicitis aguda. Se realizó apendicectomía mediante incisión de Mc Burney. El estudio anatomopatológico e inmunomarcación informó neoplasia neuroendocrina bien diferenciada y neoplasia epitelial mucinosa de bajo grado. Se realizó seguimiento con marcadores tumorales postquirúrgicos con resultados normales, además de tomografía computada y colonoscopia postquirúrgicos normales. Discusión: El tumor de colisión apendicular es muy poco frecuente. Generalmente el diagnóstico se realiza con el estudio anatomopatológico y plantea grandes desafíos para el control, ya que no existe consenso de cómo realizar el seguimiento postquirúrgico Conclusión: Se debe investigar más al respecto para contar con recomendaciones de vigilancia para dicha enfermedad. Introdução: Um tumor de colisão apendicular é definido como a presença de dois tipos histologicamente distintos de tumores no apêndice, sem transição entre eles. Os tumores apendiculares são raros, sendo as neoplasias epiteliais e neuroendócrinas as mais comuns. Objetivo: Apresentar o caso de um paciente com diagnóstico de tumor de colisão apendicular que se apresentou como apendicite aguda. Caso clínico: Mulher de 35 anos, consultada por dor epigástrica de 24 horas de evolução, com migração para a fossa ilíaca direita, de tipo contínuo. O exame de sangue mostrou leucocitose com neutrofilia e um ultrassom a favor da apendicite aguda. Apendicectomia foi realizada. O estudo de patologia e imunocoloração relatou neoplasia neuroendócrina bem diferenciada e neoplasia epitelial mucinosa de baixo grau. Discussão: O tumor de colisão apendicular é muito raro. O diagnóstico geralmente é feito com o estudo patológico e apresenta grandes desafios para o controle, uma vez que não há consenso sobre como realizar o acompanhamento pós-cirúrgico. Conclusão: Mais pesquisas devem ser feitas nesse sentido para ter recomendações de vigilância para esta doença. Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2020-04-07 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion text/html application/pdf https://revistas.unc.edu.ar/index.php/med/article/view/25071 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 77 No. 2 (2020); 113-116 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 77 Núm. 2 (2020); 113-116 Revista da Faculdade de Ciências Médicas de Córdoba; v. 77 n. 2 (2020); 113-116 1853-0605 0014-6722 10.31053/1853.0605.v77.n2 spa https://revistas.unc.edu.ar/index.php/med/article/view/25071/29618 https://revistas.unc.edu.ar/index.php/med/article/view/25071/29882 Derechos de autor 2020 Universidad Nacional de Córdoba |