Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy

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Diffuse plane xanthomatosis is an uncommon subtype of non-Langerhans histiocytosis. We report a case of a 78 year-old woman with a history of monoclonal gammopathy of undetermined significance and diffuse plane xanthomatosis since 1995. She consulted for malaise and died four days after admission. A...

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Autores principales: Bürgesser, María Virginia, Calafat, Patricia, Diller, Ana
Formato: Artículo revista
Lenguaje:Español
Publicado: Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2011
Materias:
diffuse plane xanthomatosis
monoclonal gammopathy
neoplasm
lymphoplasmacytic lymphoma
solid tumor
xantomatosis plana difusa
gammapatía monoclonal
neoplasia
linfoma linfoplasmocítico
tumor sólido
Acceso en línea:https://revistas.unc.edu.ar/index.php/med/article/view/21538
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Revistas de la UNC de Universidad Nacional de Córdoba
id I10-R10-article-21538
record_format ojs
spelling I10-R10-article-215382019-05-20T10:49:17Z Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy Xantomatosis plana difusa asociada a tumor hematológico y neoplasia sólida. Hallazgos de una autopsia Bürgesser, María Virginia Calafat, Patricia Diller, Ana diffuse plane xanthomatosis monoclonal gammopathy neoplasm lymphoplasmacytic lymphoma solid tumor xantomatosis plana difusa gammapatía monoclonal neoplasia linfoma linfoplasmocítico tumor sólido Diffuse plane xanthomatosis is an uncommon subtype of non-Langerhans histiocytosis. We report a case of a 78 year-old woman with a history of monoclonal gammopathy of undetermined significance and diffuse plane xanthomatosis since 1995. She consulted for malaise and died four days after admission. Autopsy was requested. Findings were diffuse plane xanthomatosis with extensive involvement of internal organs, lymphoplasmacytic lymphoma and cecal adenocarcinoma. Final event was acute bronchopneumonia. This entity is a subtype of histiocytosis. It affects skin and involves mucous membranes in 40% of the cases. Extracutaneous extension has been reported. It is usually associated with haematologic disorders. In this case, the patient had a lymphoplasmacytic lymphoma and colonic adenocarcinoma. We highlight the importance of recognition its association with monoclonal gammopathies and solid tumors in order to make a proper follow up of patients. La xantomatosis plana difusa es un subtipo de histiocitosis no Langerhans infrecuente. Se presenta el caso de una mujer de 78 años con antecedentes de gammapatía monoclonal de significado incierto y de xantomatosis plana difusa desde 1995. Consultó por deterioro del estado general. Falleció al cuarto día del ingreso. Se solicitó autopsia. Los hallazgos fueron xantomatosis plana difusa con compromiso extenso de órganos internos, linfoma linfoplasmacítico y adenocarcinoma de ciego. El evento final fue bronconeumonía aguda. Esta entidad corresponde a un subtipo de histiocitosis. Afecta piel y compromete mucosas en un 40%. La extensión extracutánea ha sido descripta y suele asociarse con enfermedades hematológicas. En este caso, se presenta junto a un linfoma linfoplasmacítico y a un adenocarcinoma colónico. Es importante reconocer su asociación con gammapatías monoclonales y con tumores sólidos y realizar un seguimiento adecuado. Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2011-07-03 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf https://revistas.unc.edu.ar/index.php/med/article/view/21538 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 68 No. 2 (2011); 65-69 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 68 Núm. 2 (2011); 65-69 Revista da Faculdade de Ciências Médicas de Córdoba; v. 68 n. 2 (2011); 65-69 1853-0605 0014-6722 10.31053/1853.0605.v68.n2 spa https://revistas.unc.edu.ar/index.php/med/article/view/21538/21264 Derechos de autor 2018 Universidad Nacional de Córdoba
institution Universidad Nacional de Córdoba
institution_str I-10
repository_str R-10
container_title_str Revistas de la UNC
language Español
format Artículo revista
topic diffuse plane xanthomatosis
monoclonal gammopathy
neoplasm
lymphoplasmacytic lymphoma
solid tumor
xantomatosis plana difusa
gammapatía monoclonal
neoplasia
linfoma linfoplasmocítico
tumor sólido
spellingShingle diffuse plane xanthomatosis
monoclonal gammopathy
neoplasm
lymphoplasmacytic lymphoma
solid tumor
xantomatosis plana difusa
gammapatía monoclonal
neoplasia
linfoma linfoplasmocítico
tumor sólido
Bürgesser, María Virginia
Calafat, Patricia
Diller, Ana
Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
topic_facet diffuse plane xanthomatosis
monoclonal gammopathy
neoplasm
lymphoplasmacytic lymphoma
solid tumor
xantomatosis plana difusa
gammapatía monoclonal
neoplasia
linfoma linfoplasmocítico
tumor sólido
author Bürgesser, María Virginia
Calafat, Patricia
Diller, Ana
author_facet Bürgesser, María Virginia
Calafat, Patricia
Diller, Ana
author_sort Bürgesser, María Virginia
title Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_short Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_full Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_fullStr Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_full_unstemmed Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_sort diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. findings of an autopsy
description Diffuse plane xanthomatosis is an uncommon subtype of non-Langerhans histiocytosis. We report a case of a 78 year-old woman with a history of monoclonal gammopathy of undetermined significance and diffuse plane xanthomatosis since 1995. She consulted for malaise and died four days after admission. Autopsy was requested. Findings were diffuse plane xanthomatosis with extensive involvement of internal organs, lymphoplasmacytic lymphoma and cecal adenocarcinoma. Final event was acute bronchopneumonia. This entity is a subtype of histiocytosis. It affects skin and involves mucous membranes in 40% of the cases. Extracutaneous extension has been reported. It is usually associated with haematologic disorders. In this case, the patient had a lymphoplasmacytic lymphoma and colonic adenocarcinoma. We highlight the importance of recognition its association with monoclonal gammopathies and solid tumors in order to make a proper follow up of patients.
publisher Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
publishDate 2011
url https://revistas.unc.edu.ar/index.php/med/article/view/21538
work_keys_str_mv AT burgessermariavirginia diffuseplabexanthomatosisassociatedwithhaematologicdisorderandsolidtumorfindingsofanautopsy
AT calafatpatricia diffuseplabexanthomatosisassociatedwithhaematologicdisorderandsolidtumorfindingsofanautopsy
AT dillerana diffuseplabexanthomatosisassociatedwithhaematologicdisorderandsolidtumorfindingsofanautopsy
AT burgessermariavirginia xantomatosisplanadifusaasociadaatumorhematologicoyneoplasiasolidahallazgosdeunaautopsia
AT calafatpatricia xantomatosisplanadifusaasociadaatumorhematologicoyneoplasiasolidahallazgosdeunaautopsia
AT dillerana xantomatosisplanadifusaasociadaatumorhematologicoyneoplasiasolidahallazgosdeunaautopsia
first_indexed 2022-08-20T01:26:09Z
last_indexed 2022-08-20T01:26:09Z
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