Putative association of a mutant ROM1 allele with retinitis pigmentosa

Retinitis pigmentosa (RP) is a clinically and genetically heterogeneous form of retinal degeneration. Several genes and loci have been shown to be involved in the disease, although each of them only accounts for a few cases. Mutations in the gene encoding ROM1, a rod-specific protein, have been puta...

Descripción completa

Guardado en:
Detalles Bibliográficos
Autor principal: Martínez-Mir, A.
Otros Autores: Vilela, C., Bayés, M., Valverde, D., Dain, L., Beneyto, M., Marco, M., Baiget, M., Grinberg, D., Balcells, S., Gonzàlez-Duarte, R., Vilaseliu, L.
Formato: Capítulo de libro
Lenguaje:Inglés
Publicado: 1997
Acceso en línea:Registro en Scopus
DOI
Handle
Registro en la Biblioteca Digital
Aporte de:Registro referencial: Solicitar el recurso aquí
LEADER 10588caa a22011657a 4500
001 PAPER-3256
003 AR-BaUEN
005 20230518203243.0
008 190411s1997 xx ||||fo|||| 00| 0 eng|d
024 7 |2 scopus  |a 2-s2.0-1842296355 
024 7 |2 cas  |a Eye Proteins; Membrane Proteins; ROM1 protein, human 
040 |a Scopus  |b spa  |c AR-BaUEN  |d AR-BaUEN 
030 |a HUGED 
100 1 |a Martínez-Mir, A. 
245 1 0 |a Putative association of a mutant ROM1 allele with retinitis pigmentosa 
260 |c 1997 
270 1 0 |m Vilageliu, L.; Departament de Genetica, Fac. Biologia Universitat Barcelona, Av. Diagonal 645, E-08071 Barcelona, Spain; email: lluisa@porthos.bio.ub.es 
506 |2 openaire  |e Política editorial 
504 |a Bascom, R.A., Manara, S., Collins, L., Molday, R.S., Kalnins, V.I., Mcinnes, R.R., Cloning of the cDNA for a novel photoreceptor membrane protein (rom-1) identifies a disk rim protein family implicated in human retinopathies (1992) Neuron, 8, pp. 1171-1184 
504 |a Bascom, R.A., Schappert, K., McInnes, R.R., Cloning of the human and murine ROM1 genes: Genomic organization and sequence conservation (1993) Hum Mol Genet, 2, pp. 385-391 
504 |a Bascom, R.A., Liu, L., Humphries, P., Fishman, G.A., Murray, J.C., McInnes, R.R., Polymorphisms and rare sequence variants at the ROM1 locus (1993) Hum Mol Genet, 2, pp. 1975-1977 
504 |a Bascom, R.A., Liu, L., Heckenlively, J.R., Stone, E.M., McInnes, R., Mutation analysis of the ROM1 gene in retinitis pigmentosa (1995) Hum Mol Genet, 4, pp. 1895-1902. , erratum:4:2424 
504 |a Bayés, M., Valverde, D., Balcells, S., Grinberg, D., Vilageliu, L., Benítez, J., Ayuso, C., Gonzàlez-Duarte, R., Evidence against involvement of recoverin in autosomal recessive retinitis pigmentosa in 42 Spanish families (1995) Hum Genet, 96, pp. 89-94 
504 |a Bayés, M., Martínez-Mir, A., Valverde, D., Del Río, E., Vilageliu, L.L., Grinberg, D., Balcells, S., Gonzàlez-Duarte, R., Autosomal recessive retinitis pigmentosa in Spain: Evaluation of 4 genes and 2 loci involved in the disease (1996) Clin Genet, 50, pp. 380-387 
504 |a Berson, E.L., Simonoff, E.A., Dominant retinitis pigmentosa with reduced penetrance (1979) Arch Ophthalmol, 97, pp. 1286-1291 
504 |a Collins, C., Hutchinson, G., Kowbel, D., Riess, O., Weber, B., Hayden, M.R., The human beta-subunit of rod photoreceptor cGMP phosphodiesterase - Complete retinal cDNA sequence and evidence for expression in brain (1992) Genomics, 13, pp. 698-704 
504 |a Dryja, T.P., Li, T., Molecular genetics of retinitis pigmentosa (1995) Hum Mol Genet, 4, pp. 1739-1743 
504 |a Evans, K., Almaghtheh, M., Fitzke, F.W., Moore, A.T., Jay, M., Inglehearn, C.F., Arden, G.B., Bird, A.C., Bimodal expressivity in dominant retinitis pigmentosa genetically linked to chromosome 19q (1995) Br J Ophthalmol, 79, pp. 841-846 
504 |a Hahn, L.B., Berson, E.L., Dryja, T.P., Evaluation of the gene encoding the gamma subunit of rod phosphodiesterase in retinitis pigmentosa (1994) Invest Ophthalmol Vis Sci, 35, pp. 1077-1082 
504 |a Heckenlively, J.R., Yoser, S.L., Friedman, L.H., Oversier, J.J., Clinical findings and common symptoms in retinitis pigmentosa (1988) Am J Ophthalmol, 105, pp. 504-511 
504 |a Kajiwara, K., Berson, E.L., Dryja, T., Digenic retinitis pigmentosa due to mutations at the unlinked peripherin/RDS and ROM1 loci (1994) Science, 264, pp. 1604-1608 
504 |a Keen, T.J., Inglehearn, C.F., Lester, D.H., Bashir, R., Jay, M., Bird, A.C., Jay, B., Bhattacharya, S.S., Autosomal dominant retinitis-pigmentosa - Four new mutations in rhodopsin, one of them in the retinal attachment site (1991) Genomics, 11, pp. 199-205 
504 |a Kim, S.K., Haines, J.L., Berson, E.L., Dryja, T.P., Nonallelic heterogeneity in autosomal dominant retinitis pigmentosa with incomplete penetrance (1994) Genomics, 22, pp. 659-660 
504 |a Kim, R.Y., Fitzke, F.W., Moore, A.T., Jay, M., Inglehearn, C., Arden, G.B., Bhattacharya, S.S., Bird, A.C., Autosomal dominant retinitis pigmentosa mapping to chromosome 7p exhibits variable expression (1995) Br J Ophthalmol, 79, pp. 23-27 
504 |a Kumar-Singh, R., Jordan, S.A., Farrar, G.J., Humphries, P., Poly (T/A) polymorphism at the human retinal degeneration slow (RDS) locus (1991) Nucleic Acids Res, 19, p. 5800 
504 |a Miller, S.A., Dyke, D.D., Polesky, H.F., A simple salting out procedure for extracting DNA from human nucleated cells (1988) Nucleic Acids Res, 16, p. 1215 
504 |a Moritz, O.L., Molday, R.S., Molecular cloning, membrane topology, and localization of bovine rom-1 in rod and cone photoreceptor cells (1996) Invest Ophthalmol Vis Sci, 37, pp. 352-362 
504 |a Piriev, N.I., Khramtsov, N.V., Lipkin, V.M., Cloning and characterization of the gene encoding the cGMP-phosphodiesterase gamma-subunit of human rod photoreceptor cells (1994) Gene, 151, pp. 297-301 
504 |a Riess, O., Noerremoelle, A., Weber, B., Musarella, M.A., Hayden, M.R., The search for mutations in the gene for the beta-subunit of the cGMP phosphodiesterase (PDEB) in patients with autosomal recessive retinitis-pigmentosa (1992) Am J Hum Genet, 51, pp. 755-762 
504 |a Sakuma, H., Inana, G., Murakami, A., Yajima, T., Weleber, R.G., Murphey, W.H., Gass, J.D.M., Jacobson, S.G., A heterozygous putative null mutation in ROM-1 without a mutation in peripherin/RDS in a family with retinitis pigmentosa (1995) Genomics, 27, pp. 384-386 
504 |a Sheffield, V.C., Beck, J.S., Nichols, B., Cousineau, A., Lidral, A.C., Stone, E.M., Detection of multiallele polymorphisms within gene sequences by GC-clamped denaturing gradient gel electrophoresis (1992) Am J Hum Genet, 50, pp. 567-575 
504 |a Travis, G.H., Christerson, L., Danielson, P.E., Klisak, I., Sparkes, R.S., Hahn, L.B., Dryja, T.P., Sutcliffe, J.G., The human retinal degeneration slow (RDS) gene - Chromosome assignment and structure of the messenger RNA (1991) Genomics, 10, pp. 733-739 
504 |a Xu, S.Y., Nakazawa, M., Tamai, M., Gal, A., Autosomal dominant retinitis pigmentosa locus on chromosome 19q in a Japanese family (1995) J Med Genet, 32, pp. 915-916 
520 3 |a Retinitis pigmentosa (RP) is a clinically and genetically heterogeneous form of retinal degeneration. Several genes and loci have been shown to be involved in the disease, although each of them only accounts for a few cases. Mutations in the gene encoding ROM1, a rod-specific protein, have been putatively associated with several forms of RP. Here we describe a double-mutant allele of this gene, P60T and T108M, present in two affected sibs and also in two healthy members of a Spanish RP family. The same double-mutant allele was previously considered to be responsible for autosomal dominant RP in one family. We now report data that question the potential pathogenicity of these two ROM1 mutations.  |l eng 
536 |a Detalles de la financiación: Generalitat de Catalunya 
536 |a Detalles de la financiación: Universidad de Buenos Aires 
536 |a Detalles de la financiación: Comisión Interministerial de Ciencia y Tecnología, SAF96-0329, SAF93-0479-062- 01 
536 |a Detalles de la financiación: Acknowledgements We are indebted to Dr. A. Swaroop for providing the NRL gene sequence and primers. We appreciate the invaluable contribution of Lola Sánchez in collecting the samples and her enthusiasm throughout this work. We thank family members for their cooperation and patience when taking the tests. Robin Rycroft revised the English; we greatly appreciate his help. This work was supported by Spanish CICYT (SAF93-0479-062- 01; SAF96-0329) and the “Federación de Asociaciones de Afecta-dos de Retinosis Pigmentaria del Estado Español” (FAARPE). A. Martínez-Mir and M. Bayés are recipients of fellowships from the “Generalitat de Catalunya” and L. Dain received an R. H. Thal-mann fellowship from Universidad de Buenos Aires. 
593 |a Departament de Genètica, Facultat de Biologia, Universitat de Barcelona, Av. Diagonal 645, E-08071 Barcelona, Spain 
593 |a Servicio de Neurofisiologia, Hospital Universitario La Fe, E-46009 Valencia, Spain 
593 |a Unitat de Genètica Molecular, Hospital de la Santa Creu i Sant Pau, E-08025 Barcelona, Spain 
593 |a Unidad de Genética, Hospital Universitario La Fe, E-46009 Valencia, Spain 
593 |a Servicio de Oftalmología, Hosp. Clínico Universitario, Valencia, Spain 
593 |a Depto. de Diagnostico Genetico, INGEM y FCEN UBA, Buenos Aires, Argentina 
690 1 0 |a MEMBRANE PROTEIN 
690 1 0 |a MUTANT PROTEIN 
690 1 0 |a ARTICLE 
690 1 0 |a CASE REPORT 
690 1 0 |a CONTROLLED STUDY 
690 1 0 |a FEMALE 
690 1 0 |a GENE MUTATION 
690 1 0 |a GENETIC HETEROGENEITY 
690 1 0 |a HUMAN 
690 1 0 |a HUMAN CELL 
690 1 0 |a PRIORITY JOURNAL 
690 1 0 |a RETINA ROD OUTER SEGMENT 
690 1 0 |a RETINITIS PIGMENTOSA 
690 1 0 |a ADOLESCENT 
690 1 0 |a ADULT 
690 1 0 |a ALLELES 
690 1 0 |a EYE PROTEINS 
690 1 0 |a FEMALE 
690 1 0 |a HUMANS 
690 1 0 |a MALE 
690 1 0 |a MEMBRANE PROTEINS 
690 1 0 |a MIDDLE AGED 
690 1 0 |a PEDIGREE 
690 1 0 |a POLYMERASE CHAIN REACTION 
690 1 0 |a POLYMORPHISM, SINGLE-STRANDED CONFORMATIONAL 
690 1 0 |a RETINITIS PIGMENTOSA 
690 1 0 |a ROD OUTER SEGMENTS 
700 1 |a Vilela, C. 
700 1 |a Bayés, M. 
700 1 |a Valverde, D. 
700 1 |a Dain, L. 
700 1 |a Beneyto, M. 
700 1 |a Marco, M. 
700 1 |a Baiget, M. 
700 1 |a Grinberg, D. 
700 1 |a Balcells, S. 
700 1 |a Gonzàlez-Duarte, R. 
700 1 |a Vilaseliu, L. 
773 0 |d 1997  |g v. 99  |h pp. 827-830  |k n. 6  |p HUM. GENET.  |x 03406717  |w (AR-BaUEN)CENRE-1775  |t Human Genetics 
856 4 1 |u https://www.scopus.com/inward/record.uri?eid=2-s2.0-1842296355&doi=10.1007%2fs004390050456&partnerID=40&md5=7d156d3979a0b818d8abdae46d1f16b0  |y Registro en Scopus 
856 4 0 |u https://doi.org/10.1007/s004390050456  |y DOI 
856 4 0 |u https://hdl.handle.net/20.500.12110/paper_03406717_v99_n6_p827_MartinezMir  |y Handle 
856 4 0 |u https://bibliotecadigital.exactas.uba.ar/collection/paper/document/paper_03406717_v99_n6_p827_MartinezMir  |y Registro en la Biblioteca Digital 
961 |a paper_03406717_v99_n6_p827_MartinezMir  |b paper  |c PE 
962 |a info:eu-repo/semantics/article  |a info:ar-repo/semantics/artículo  |b info:eu-repo/semantics/publishedVersion 
999 |c 64209