T-cell intestinal lymphoma in a female patient with dermatitis herpetiformis (Düring-Brocq disease) [Linfoma intestinal de células T en una paciente con dermatitis herpetiforme (Enfermedad de Dühring-Brocq)]

Dermatitis herpetiformis (DH) or Düring-Brocq disease, a particularly pruritic bullous skin disease, is part of a spectrum of gluten-sensitive disorders that includes celiac disease. The risk for lymphoma is increased in both dermatitis herpetiformis and in celiac disease, predominantly T-cell lymph...

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Autores principales: Danielo, Cristian, Consigli, Javier Enrique, Gómez Zanni, Susana, Gallerano, Verónica, Trakal, Juan José, Guidi, Andrés Emilio
Formato: Artículo
Lenguaje:Español
Publicado: 2007
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Acceso en línea:http://pa.bibdigital.ucc.edu.ar/4041/1/A_Danielo_Consigli_G%C3%B3mezZanni_Gallerano_Trakal_Guidi.pdf
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Sumario:Dermatitis herpetiformis (DH) or Düring-Brocq disease, a particularly pruritic bullous skin disease, is part of a spectrum of gluten-sensitive disorders that includes celiac disease. The risk for lymphoma is increased in both dermatitis herpetiformis and in celiac disease, predominantly T-cell lymphomas. We report the case of a patient with dermatitis herpetiformis and celiac disease who developed intestinal lymphoma.