Assessment of ataxia rating scales and cerebellar functional tests : critique and recommendations

Background: We assessed the clinimetric properties of ataxia rating scales and functional tests, and made recommendations regarding their use. Methods: A systematic literature search was conducted to identify the instruments used to rate ataxia symptoms. The identified rating scales and functio...

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Detalles Bibliográficos
Autores principales: Pérez Lloret, Santiago, Warrenburg, Bart van de, Rossi, Malco Damián, Rodríguez-Blázquez, Carmen, Zesiewicz, Theresa, Saute, Jonas A. M., Durr, Alexandra, Nishizawa, Masatoyo, Martinez-Martin, Pablo, Stebbins, Glenn T., Schrag, Anette, Skorvanek, Matej
Formato: Artículo
Lenguaje:Inglés
Publicado: Wiley 2020
Materias:
ATAXIA
DESORDENES CEREBRALES
ENSAYO CLINICO
ESCALA DE CLASIFICACION
NEUROLOGIA
Acceso en línea:https://repositorio.uca.edu.ar/handle/123456789/10858
Aporte de:
Repositorio Institucional de la Universidad Católica Argentina (UCA) de Universidad Católica Argentina
Descripción
Sumario:Background: We assessed the clinimetric properties of ataxia rating scales and functional tests, and made recommendations regarding their use. Methods: A systematic literature search was conducted to identify the instruments used to rate ataxia symptoms. The identified rating scales and functional ability tests were reviewed and ranked by the panel as “recommended,” “suggested,” or “listed” for the assessment of patients with discrete cerebellar disorders, using previously established criteria. Results: We reviewed 14 instruments (9 rating scales and 5 functional tests). “Recommended” rating scales for the assessment of symptoms severity were: for Friedreich’s ataxia, the Friedreich’s Ataxia Rating Scale, the International Cooperative Ataxia Rating Scale (ICARS), and the Scale for the Assessment and Rating of Ataxia (SARA); for spinocerebellar ataxias, ICARS and SARA; for ataxia telangiectasia: ICARS and SARA; for brain tumors, SARA; for congenital disorder of glycosylation-phosphomannomutase-2 deficiency, ICARS; for cerebellar symptoms in multiple sclerosis, ICARS; for cerebellar symptoms in multiple system atrophy: Unified Multiple System Atrophy Rating Scale and ICARS; and for fragile X–associated tremor ataxia syndrome, ICARS. “Recommended” functional tests were: for Friedreich’s ataxia, Ataxia Functional Composite Score and Composite Cerebellar Functional Severity Score; and for spinocerebellar ataxias, Ataxia Functional Composite Score, Composite Cerebellar Functional Severity Score, and SCA Functional Index.

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