Superior Cava Venous syndrome as presentation of neoplasic disease

Superior Cava Venous Syndrome (SVCS) encompasses a constellation of signsand symptoms resulting from partial or complete obstruction of blood flow through the superior vena cava (SVC) to the right atrium. Thrombosis can be caused by intrinsic (primary) or extrinsic compression (with or without secon...

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Autores principales: Pérez Maure, M, Subils, G, Peresin Paz, R, Cazaux, A, Cambursano, V H, Cortes, J R
Formato: Artículo revista
Lenguaje:Español
Publicado: Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2013
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Acceso en línea:https://revistas.unc.edu.ar/index.php/med/article/view/7407
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spelling I10-R327-article-74072024-08-27T18:19:21Z Superior Cava Venous syndrome as presentation of neoplasic disease Síndrome de vena cava superior: forma inicial de presentacion en enfermedades neoplásicas Pérez Maure, M Subils, G Peresin Paz, R Cazaux, A Cambursano, V H Cortes, J R Síndrome de Vena Cava Superior Superior Cava Venous Syndrome (SVCS) encompasses a constellation of signsand symptoms resulting from partial or complete obstruction of blood flow through the superior vena cava (SVC) to the right atrium. Thrombosis can be caused by intrinsic (primary) or extrinsic compression (with or without secondary thrombosis).The causes of SVCS can be grouped according to their etiology in non-neoplastic and neoplastic. The causes malignant correspond to 65-90% of them, thrombosis and nonmalignant conditions are another causes.The presentation may be acute, clinically characterized by dyspnea and a characteristic triad (facial, neck and arms edema, cyanosis and collateral  circulation).Early detection improves prognosis and is based on clinical data and imaging studies.We describe 8 cases where the SVCS was the first manifestation of neoplasticdiseases. Patients were predominantly of middle-aged, male, without association with consumption of tobacco and lymphoma was most frequent diagnosis Se denomina Síndrome de Vena Cava Superior (SVCS) al conjunto de signos y síntomas derivados de la obstrucción parcial o completa del flujo sanguíneo a través de la vena cava superior (VCS) hacia la aurícula derecha. Puede ser causada por trombosis intrínseca (primaria) o a compresión extrínseca (asociada o no a trombosis secundaria)Las causas de SVCS pueden ser agrupadas según su etiología en no neoplásicas y neoplásicas. Las causas malignas corresponden a un 65-90% del total de las causas, la trombosis y las condiciones no malignas son las causantes del resto de los casos.La forma de presentación puede ser aguda, caracterizándose clínicamente por disnea y la triada característica (edema en esclavina, cianosis facial y presencia de circulación colateral).La detección precoz mejora el pronóstico y se asienta sobre los datos clínicos y estudios por imágenes. Presentamos 8 casos registrados en nuestro hospital, donde el SVCS fue la manifestación inicial de enfermedades neoplásicas. En esta serie hubo predominancia de varones de edad media, sin asociación con consumo de tabaco y el diagnóstico más frecuente fue linfoma.   Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2013-12-01 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf https://revistas.unc.edu.ar/index.php/med/article/view/7407 10.31053/1853.0605.v70.n4.7407 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 70 No. 4 (2013); 226-231 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 70 Núm. 4 (2013); 226-231 Revista da Faculdade de Ciências Médicas de Córdoba; v. 70 n. 4 (2013); 226-231 1853-0605 0014-6722 10.31053/1853.0605.v70.n4 spa https://revistas.unc.edu.ar/index.php/med/article/view/7407/37264 Derechos de autor 2013 Universidad Nacional de Córdoba https://creativecommons.org/licenses/by-nc/4.0
institution Universidad Nacional de Córdoba
institution_str I-10
repository_str R-327
container_title_str Revista de la Facultad de Ciencias Médicas de Córdoba
language Español
format Artículo revista
topic Síndrome de Vena Cava Superior
spellingShingle Síndrome de Vena Cava Superior
Pérez Maure, M
Subils, G
Peresin Paz, R
Cazaux, A
Cambursano, V H
Cortes, J R
Superior Cava Venous syndrome as presentation of neoplasic disease
topic_facet Síndrome de Vena Cava Superior
author Pérez Maure, M
Subils, G
Peresin Paz, R
Cazaux, A
Cambursano, V H
Cortes, J R
author_facet Pérez Maure, M
Subils, G
Peresin Paz, R
Cazaux, A
Cambursano, V H
Cortes, J R
author_sort Pérez Maure, M
title Superior Cava Venous syndrome as presentation of neoplasic disease
title_short Superior Cava Venous syndrome as presentation of neoplasic disease
title_full Superior Cava Venous syndrome as presentation of neoplasic disease
title_fullStr Superior Cava Venous syndrome as presentation of neoplasic disease
title_full_unstemmed Superior Cava Venous syndrome as presentation of neoplasic disease
title_sort superior cava venous syndrome as presentation of neoplasic disease
description Superior Cava Venous Syndrome (SVCS) encompasses a constellation of signsand symptoms resulting from partial or complete obstruction of blood flow through the superior vena cava (SVC) to the right atrium. Thrombosis can be caused by intrinsic (primary) or extrinsic compression (with or without secondary thrombosis).The causes of SVCS can be grouped according to their etiology in non-neoplastic and neoplastic. The causes malignant correspond to 65-90% of them, thrombosis and nonmalignant conditions are another causes.The presentation may be acute, clinically characterized by dyspnea and a characteristic triad (facial, neck and arms edema, cyanosis and collateral  circulation).Early detection improves prognosis and is based on clinical data and imaging studies.We describe 8 cases where the SVCS was the first manifestation of neoplasticdiseases. Patients were predominantly of middle-aged, male, without association with consumption of tobacco and lymphoma was most frequent diagnosis
publisher Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
publishDate 2013
url https://revistas.unc.edu.ar/index.php/med/article/view/7407
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