Eosinophilic granuloma of cranial location: report of a case and bibliographic review
Introduction: Eosinophilic granuloma is an unusual benign disease that usually affects the pediatric population and young adults. It is the most benign of the diseases traditionally known as histiocytosis X that are now called Langerhans cell histiocytosis. Clinical Case: Pediatric patient with a pa...
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| Autores principales: | , , |
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| Formato: | Artículo revista |
| Lenguaje: | Español |
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Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2021
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| Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/30451 |
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I10-R327-article-30451 |
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Universidad Nacional de Córdoba |
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I-10 |
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R-327 |
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Revista de la Facultad de Ciencias Médicas de Córdoba |
| language |
Español |
| format |
Artículo revista |
| topic |
histiocytosis, langerhans-cell pediatrics temporal bone histiocitosis de células de langerhans pediatría hueso temporal histiocitose de células de langerhans pediatria osso temporal |
| spellingShingle |
histiocytosis, langerhans-cell pediatrics temporal bone histiocitosis de células de langerhans pediatría hueso temporal histiocitose de células de langerhans pediatria osso temporal Ramon y Cajal Calvo, Juan Alvarez Arranz, Enrique Zamora Lozano, Marta Eosinophilic granuloma of cranial location: report of a case and bibliographic review |
| topic_facet |
histiocytosis, langerhans-cell pediatrics temporal bone histiocitosis de células de langerhans pediatría hueso temporal histiocitose de células de langerhans pediatria osso temporal |
| author |
Ramon y Cajal Calvo, Juan Alvarez Arranz, Enrique Zamora Lozano, Marta |
| author_facet |
Ramon y Cajal Calvo, Juan Alvarez Arranz, Enrique Zamora Lozano, Marta |
| author_sort |
Ramon y Cajal Calvo, Juan |
| title |
Eosinophilic granuloma of cranial location: report of a case and bibliographic review |
| title_short |
Eosinophilic granuloma of cranial location: report of a case and bibliographic review |
| title_full |
Eosinophilic granuloma of cranial location: report of a case and bibliographic review |
| title_fullStr |
Eosinophilic granuloma of cranial location: report of a case and bibliographic review |
| title_full_unstemmed |
Eosinophilic granuloma of cranial location: report of a case and bibliographic review |
| title_sort |
eosinophilic granuloma of cranial location: report of a case and bibliographic review |
| description |
Introduction: Eosinophilic granuloma is an unusual benign disease that usually affects the pediatric population and young adults. It is the most benign of the diseases traditionally known as histiocytosis X that are now called Langerhans cell histiocytosis.
Clinical Case: Pediatric patient with a painful lump in the temporal region. The imaging tests carried out reveal the existence of an osteolytic lesion with an aggressive pattern compatible with eosinophilic granuloma. The patient underwent surgery with a conclusive definitive histological diagnosis of eosinophilic granuloma.
Discussion: Eosinophilic granuloma can affect one or multiple bones, of which the most frequent are the cranial bones, epiphyses of long bones and ribs, requiring individualized diagnosis and treatment strategies for optimal management and results, with surgical treatment of First choice.
Conclusion: Eosinophilic granuloma is an infrequent benign condition that requires a correct anamnesis and clinical examination of the patient, as well as the demonstration of the characteristic radiological images, allowing a generally accurate presumptive diagnosis to be reached that in most cases can be considered definitive. |
| publisher |
Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
| publishDate |
2021 |
| url |
https://revistas.unc.edu.ar/index.php/med/article/view/30451 |
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I10-R327-article-304512021-07-07T13:29:31Z Eosinophilic granuloma of cranial location: report of a case and bibliographic review Granuloma eosinófilo de localización craneal: reporte de un caso y revisión bibliográfica Granuloma eosinofílico de localização craniana: relato de um caso e revisão bibliográfica Ramon y Cajal Calvo, Juan Alvarez Arranz, Enrique Zamora Lozano, Marta histiocytosis, langerhans-cell pediatrics temporal bone histiocitosis de células de langerhans pediatría hueso temporal histiocitose de células de langerhans pediatria osso temporal Introduction: Eosinophilic granuloma is an unusual benign disease that usually affects the pediatric population and young adults. It is the most benign of the diseases traditionally known as histiocytosis X that are now called Langerhans cell histiocytosis. Clinical Case: Pediatric patient with a painful lump in the temporal region. The imaging tests carried out reveal the existence of an osteolytic lesion with an aggressive pattern compatible with eosinophilic granuloma. The patient underwent surgery with a conclusive definitive histological diagnosis of eosinophilic granuloma. Discussion: Eosinophilic granuloma can affect one or multiple bones, of which the most frequent are the cranial bones, epiphyses of long bones and ribs, requiring individualized diagnosis and treatment strategies for optimal management and results, with surgical treatment of First choice. Conclusion: Eosinophilic granuloma is an infrequent benign condition that requires a correct anamnesis and clinical examination of the patient, as well as the demonstration of the characteristic radiological images, allowing a generally accurate presumptive diagnosis to be reached that in most cases can be considered definitive. Introducción: El granuloma eosinófilo es una enfermedad benigna poco usual que suele afectar a la población pediátrica y adultos jóvenes. Es la afección más benigna de las enfermedades tradicionalmente conocidas como histiocitosis X que en la actualidad reciben la denominación de histiocitosis de células de Langerhans. Caso Clínico: Paciente pediátrico con bultoma doloroso en región temporal. Las pruebas de imagen realizadas ponen de manifiesto la existencia de una lesión osteolítica con patrón de agresividad compatible con granuloma eosinófilo. El paciente es intervenido mediante cirugía con diagnóstico histológico definitivo concluyente de granuloma eosinófilo. Discusión: El granuloma eosinófilo puede afectar a uno o múltiples huesos, de los cuáles los más frecuentes son los huesos craneales, epífisis de huesos largos y costillas, precisando estrategias de diagnóstico y tratamiento individualizadas para un manejo y resultado óptimo, siendo el tratamiento quirúrgico de primera elección. Conclusión: El granuloma eosinófilo es un cuadro benigno infrecuente que requiere de una correcta anamnesis y exploración clínica del paciente, así como la demostración de las imágenes radiológicas características, permitiendo llegar a un diagnóstico de presunción generalmente certero que en la mayoría de ocasiones se puede considerar definitivo. Introdução: O granuloma eosinofílico é uma doença benigna incomum que geralmente afeta a população pediátrica e adultos jovens. É a mais benigna das doenças tradicionalmente conhecidas como histiocitose X, que agora são denominadas histiocitose de células de Langerhans. Caso Clínico: Paciente pediátrico com nódulo doloroso em região temporal. Os exames de imagem realizados revelam a existência de lesão osteolítica de padrão agressivo compatível com granuloma eosinofílico. O paciente foi submetido a cirurgia com diagnóstico histológico definitivo conclusivo de granuloma eosinofílico. Discussão: O granuloma eosinofílico pode acometer um ou vários ossos, sendo os mais frequentes os ossos cranianos, epífises de ossos longos e costelas, exigindo diagnóstico individualizado e estratégias de tratamento para manejo e resultados ideais, com tratamento cirúrgico de Primeira escolha. Conclusão: O granuloma eosinofílico é uma condição benigna infrequente que requer a correta anamnese e exame clínico do paciente, bem como a demonstração das imagens radiológicas características, permitindo chegar a um diagnóstico presuntivo geralmente acurado que na maioria dos casos pode ser considerado definitivo. Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2021-03-12 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion application/pdf text/html https://revistas.unc.edu.ar/index.php/med/article/view/30451 10.31053/1853.0605.v78.n1.30451 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 78 No. 1 (2021); 48-51 Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 78 Núm. 1 (2021); 48-51 Revista da Faculdade de Ciências Médicas de Córdoba; v. 78 n. 1 (2021); 48-51 1853-0605 0014-6722 10.31053/1853.0605.v78.n1 spa https://revistas.unc.edu.ar/index.php/med/article/view/30451/33299 https://revistas.unc.edu.ar/index.php/med/article/view/30451/33266 Derechos de autor 2021 Universidad Nacional de Córdoba http://creativecommons.org/licenses/by-nc/4.0 |