Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
Diffuse plane xanthomatosis is an uncommon subtype of non-Langerhans histiocytosis. We report a case of a 78 year-old woman with a history of monoclonal gammopathy of undetermined significance and diffuse plane xanthomatosis since 1995. She consulted for malaise and died four days after admission. A...
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Formato: | Artículo revista |
Lenguaje: | Español |
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Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
2011
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Acceso en línea: | https://revistas.unc.edu.ar/index.php/med/article/view/21538 |
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I10-R10article-21538 |
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Universidad Nacional de Córdoba |
institution_str |
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Revistas de la UNC |
language |
Español |
format |
Artículo revista |
topic |
diffuse plane xanthomatosis monoclonal gammopathy neoplasm lymphoplasmacytic lymphoma solid tumor xantomatosis plana difusa gammapatía monoclonal neoplasia linfoma linfoplasmocítico tumor sólido |
spellingShingle |
diffuse plane xanthomatosis monoclonal gammopathy neoplasm lymphoplasmacytic lymphoma solid tumor xantomatosis plana difusa gammapatía monoclonal neoplasia linfoma linfoplasmocítico tumor sólido Bürgesser, María Virginia Calafat, Patricia Diller, Ana Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy |
topic_facet |
diffuse plane xanthomatosis monoclonal gammopathy neoplasm lymphoplasmacytic lymphoma solid tumor xantomatosis plana difusa gammapatía monoclonal neoplasia linfoma linfoplasmocítico tumor sólido |
author |
Bürgesser, María Virginia Calafat, Patricia Diller, Ana |
author_facet |
Bürgesser, María Virginia Calafat, Patricia Diller, Ana |
author_sort |
Bürgesser, María Virginia |
title |
Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy |
title_short |
Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy |
title_full |
Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy |
title_fullStr |
Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy |
title_full_unstemmed |
Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy |
title_sort |
diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. findings of an autopsy |
description |
Diffuse plane xanthomatosis is an uncommon subtype of non-Langerhans histiocytosis. We report a case of a 78 year-old woman with a history of monoclonal gammopathy of undetermined significance and diffuse plane xanthomatosis since 1995. She consulted for malaise and died four days after admission. Autopsy was requested. Findings were diffuse plane xanthomatosis with extensive involvement of internal organs, lymphoplasmacytic lymphoma and cecal adenocarcinoma. Final event was acute bronchopneumonia. This entity is a subtype of histiocytosis. It affects skin and involves mucous membranes in 40% of the cases. Extracutaneous extension has been reported. It is usually associated with haematologic disorders. In this case, the patient had a lymphoplasmacytic lymphoma and colonic adenocarcinoma. We highlight the importance of recognition its association with monoclonal gammopathies and solid tumors in order to make a proper follow up of patients. |
publisher |
Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología |
publishDate |
2011 |
url |
https://revistas.unc.edu.ar/index.php/med/article/view/21538 |
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Revistas |
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