Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy

Diffuse plane xanthomatosis is an uncommon subtype of non-Langerhans histiocytosis. We report a case of a 78 year-old woman with a history of monoclonal gammopathy of undetermined significance and diffuse plane xanthomatosis since 1995. She consulted for malaise and died four days after admission. A...

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Autores principales: Bürgesser, María Virginia, Calafat, Patricia, Diller, Ana
Formato: Artículo revista
Lenguaje:Español
Publicado: Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2011
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Acceso en línea:https://revistas.unc.edu.ar/index.php/med/article/view/21538
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id I10-R10article-21538
record_format ojs
institution Universidad Nacional de Córdoba
institution_str I-10
repository_str R-10
container_title_str Revistas de la UNC
language Español
format Artículo revista
topic diffuse plane xanthomatosis
monoclonal gammopathy
neoplasm
lymphoplasmacytic lymphoma
solid tumor
xantomatosis plana difusa
gammapatía monoclonal
neoplasia
linfoma linfoplasmocítico
tumor sólido
spellingShingle diffuse plane xanthomatosis
monoclonal gammopathy
neoplasm
lymphoplasmacytic lymphoma
solid tumor
xantomatosis plana difusa
gammapatía monoclonal
neoplasia
linfoma linfoplasmocítico
tumor sólido
Bürgesser, María Virginia
Calafat, Patricia
Diller, Ana
Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
topic_facet diffuse plane xanthomatosis
monoclonal gammopathy
neoplasm
lymphoplasmacytic lymphoma
solid tumor
xantomatosis plana difusa
gammapatía monoclonal
neoplasia
linfoma linfoplasmocítico
tumor sólido
author Bürgesser, María Virginia
Calafat, Patricia
Diller, Ana
author_facet Bürgesser, María Virginia
Calafat, Patricia
Diller, Ana
author_sort Bürgesser, María Virginia
title Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_short Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_full Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_fullStr Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_full_unstemmed Diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. Findings of an autopsy
title_sort diffuse plabe xanthomatosis associated with haematologic disorder and solid tumor. findings of an autopsy
description Diffuse plane xanthomatosis is an uncommon subtype of non-Langerhans histiocytosis. We report a case of a 78 year-old woman with a history of monoclonal gammopathy of undetermined significance and diffuse plane xanthomatosis since 1995. She consulted for malaise and died four days after admission. Autopsy was requested. Findings were diffuse plane xanthomatosis with extensive involvement of internal organs, lymphoplasmacytic lymphoma and cecal adenocarcinoma. Final event was acute bronchopneumonia. This entity is a subtype of histiocytosis. It affects skin and involves mucous membranes in 40% of the cases. Extracutaneous extension has been reported. It is usually associated with haematologic disorders. In this case, the patient had a lymphoplasmacytic lymphoma and colonic adenocarcinoma. We highlight the importance of recognition its association with monoclonal gammopathies and solid tumors in order to make a proper follow up of patients.
publisher Universidad Nacional Cba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
publishDate 2011
url https://revistas.unc.edu.ar/index.php/med/article/view/21538
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